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Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien van den Bosch Erasmus MC, Thoraxcenter, Rotterdam, The Netherlands

Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

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Page 1: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Echocardiographic assessment of

after Rastelli operation

Multimodality Imaging in ACHD and PH

Annemien van den Bosch

Erasmus MC, Thoraxcenter, Rotterdam, The Netherlands

Page 2: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Rastelli surgical technique

Rastelli operation is performed in patients with a variety of

congenital abnormalities

Common theme being the presence of a VSD

- Double outlet right ventricle with VSD

- TGA with VSD

- Truncus arteriosus

Page 3: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Rastelli surgical technique

Patch across the native VSD, to deviate blood from the LV to the aorta

VSDs which are committed to the great arteries fare better than

remotely located VSDs, which are difficult to use in the re-routing of LV

outflow Courtesy of Dr Hans Hamer

Page 4: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Rastelli surgical technique

Native PV is disconnected proximally and a valved RV

to PA conduit is inserted

The location of the conduit is usually very anteriorly in

close proximity to the sternum

Courtesy of Dr Hans Hamer

Page 5: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Post-operative Sequelae

LV outflow obstruction

VSD patch leak

Aortic root dilatation

RV-PA conduit dysfunction

Bi-ventricular dysfunction

Page 6: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Key views specific to Rastelli repair

Aorta remains in its anterior position and LV flow is

through the VSD

LVOT becomes elongated and sometimes acutely

angulated

Page 7: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Elongated and angulated LVOT

Elongated LVOT has increased musculature at the VSD

site which can cause LV outflow obstruction

It is important to identify LVOT obstruction

Page 8: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Key views specific to Rastelli repair

Residual patch leak

Page 9: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

The patch re-routes the flow from the LV to the

anterior aorta, and so can be quite long

Search for residual VSDs

Page 10: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Key views specific to Rastelli repair

RV-AP conduit dysfunction

This is usually positioned right underneath the

sternum and requires very high parasternal views

Page 11: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Longterm consequences

are significant

regurgitation and/or

stenosis

RV-AP conduit

Vmax 3.6 m/s

Page 12: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

RV-AP conduit

Longterm consequences

are significant

regurgitation and/or

stenosis

Enddiastolic antegrade flow

Page 13: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

The conduit is long and narrow at one end, hence

assessing the length of the conduit is important

and may require multiple views

SMPI for RV-AP conduit

Page 14: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Estimate of RV systolic pressure

RV pressure estimation using TR jet may help

determine the clinical significance

Page 15: Echocardiographic assessment of after Rastelli operation documents/Annemien … · Echocardiographic assessment of after Rastelli operation Multimodality Imaging in ACHD and PH Annemien

Rastelli repair report

Clearly state the original anatomy. Rastelli operations can

be used for other anatomies as well as dTGA.

VSD patch integrity

LV outflow haemodynamics

Aortic root size

RV-PA conduit haemodynamics & assess for regurgitation

Estimate of RV systolic pressure