6
ICD-9 Code Diagnoses ICD-10 Code Behavioral/Cognitive Syndromes 294.8 Amnestic Disorder F04 294.9 Cognitive Disorder F09 312.9 Behavior Disorder F91.9 314.01 Attention Deficit Hyperactivity Disorder F90.9 Cerebral Degeneration 294.20 Dementia F03.90 331.0 Alzheimer’s Disease G30.9 331.11 Pick’s Disease G31.01 331.19 Frontal Dementia G31.09 331.81 Reye’s Syndrome G93.7 780.09 Delirium R41.0 Cerebral Lobe Dysfunction 780.93 Amnesia R41.3 784.3 Aphasia R47.01 784.69 Agnosia R48.1 784.69 Apraxia R48.2 Cerebrovascular Diseases 434.01 Thrombotic Stroke I63.9 434.11 Embolic Stroke I63.9 435.9 Transient Ischemic Attack G45.9 Cranial Nerve Disorders 352.9 Cranial Nerve Disorder G52.9 Developmental Delay 270.0 Amino Acid Transport Disorder Disorders Of Amino-Acid Transport, Unspecified E72.00 Cystinuria E72.01 Cystinosis E72.04 Other Disorders Of Amino-Acid Transport E72.09 270.1 Phenylketonuria [PKU] Classical Phenylketonuria E70.0 271.0 Glycogenosis Disorders Of Amino-Acid Transport, Unspecified E72.00 Cystinuria E72.01 Cystinosis E72.04 Other Disorders Of Amino-Acid Transport E72.09 Diagnostic Services ICD-9 Code Diagnoses ICD-10 Code 277.5 Mucopolysaccharidosis Other Mucopolysaccharidoses E76.29 Mucopolysaccharidosis, Unspecified E76.3 299.00 - 299.01 Autistic Disorder F84.0 299.10 - 299.11 Childhood Disintegrative Disorder F84.3 299.80 - 299.81 Other Specified Pervasive Developmental Disorders (Asperger Syndrome) Asperger's Syndrome F84.5 Other Pervasive Developmental Disorders F84.8 317 Mild Intellectual Disabilities F70 318.0 - 318.2 Other Specified Intellectual Disabilities Moderate Intellectual Disabilities F71 Severe Intellectual Disabilities F72 Profound Intellectual Disabilities F73 319 Unspecified Intellectual Disabilities F79 759.7 Multiple Congenital Anomalies, So Described Q89.7 759.83 Fragile X Syndrome Q99.2 759.89 Other Specified Anomalies Q87.89 Other Specified Congenital Malformation Syndromes, Not Elsewhere Classified Q89.8 Other specified congenital malformations 759.9 Congenital Anomaly, Unspecified Q89.9 783.42 Delayed Milestones R62.0 Genetic Disorders 270.1 Phenylketonuria E70.1 272.7 Neiman Pick Disease E75.249 272.7 Lysosomal Disorders (Gaucher, Fabry, Pompe, Etc.) 275.1 Wilson’s Disease E83.01 330.0 Leukodystrophy E75.29 330.1 Tay Sach’s Disease E75.02 Headache Disorders 307.81 Tension Headache G44.209 339.00 Cluster Headaches G44.009 346.00 Migraine Headache With Aura G43.109 ICD-9-CM to ICD-10-CM Codes for Neurology

ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

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Page 1: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

ICD-9 Code

DiagnosesICD-10Code

Behavioral/Cognitive Syndromes

294.8 Amnestic Disorder F04

294.9 Cognitive Disorder F09

312.9 Behavior Disorder F91.9

314.01 Attention Deficit Hyperactivity Disorder F90.9

Cerebral Degeneration

294.20 Dementia F03.90

331.0 Alzheimer’s Disease G30.9

331.11 Pick’s Disease G31.01

331.19 Frontal Dementia G31.09

331.81 Reye’s Syndrome G93.7

780.09 Delirium R41.0

Cerebral Lobe Dysfunction

780.93 Amnesia R41.3

784.3 Aphasia R47.01

784.69 Agnosia R48.1

784.69 Apraxia R48.2

Cerebrovascular Diseases

434.01 Thrombotic Stroke I63.9

434.11 Embolic Stroke I63.9

435.9 Transient Ischemic Attack G45.9

Cranial Nerve Disorders

352.9 Cranial Nerve Disorder G52.9

Developmental Delay

270.0 Amino Acid Transport DisorderDisorders Of Amino-Acid Transport, Unspecified E72.00

Cystinuria E72.01

Cystinosis E72.04 Other Disorders Of Amino-Acid Transport E72.09

270.1 Phenylketonuria [PKU]

Classical Phenylketonuria E70.0

271.0 GlycogenosisDisorders Of Amino-Acid Transport, Unspecified E72.00

Cystinuria E72.01

Cystinosis E72.04 Other Disorders Of Amino-Acid Transport E72.09

Diagnostic Services

ICD-9 Code

DiagnosesICD-10Code

277.5 Mucopolysaccharidosis

Other Mucopolysaccharidoses E76.29

Mucopolysaccharidosis, Unspecified E76.3 299.00 - 299.01 Autistic Disorder F84.0

299.10 - 299.11 Childhood Disintegrative Disorder F84.3

299.80 - 299.81

Other Specified Pervasive Developmental Disorders (Asperger Syndrome)Asperger's Syndrome F84.5 Other Pervasive Developmental Disorders F84.8

317 Mild Intellectual Disabilities F70318.0 - 318.2

Other Specified Intellectual DisabilitiesModerate Intellectual Disabilities F71

Severe Intellectual Disabilities F72

Profound Intellectual Disabilities F73

319 Unspecified Intellectual Disabilities F79

759.7 Multiple Congenital Anomalies, So Described Q89.7

759.83 Fragile X Syndrome Q99.2

759.89 Other Specified Anomalies Q87.89 Other Specified Congenital Malformation Syndromes, Not Elsewhere Classified

Q89.8

Other specified congenital malformations

759.9 Congenital Anomaly, Unspecified Q89.9

783.42 Delayed Milestones R62.0

Genetic Disorders

270.1 Phenylketonuria E70.1

272.7 Neiman Pick Disease E75.249

272.7 Lysosomal Disorders (Gaucher, Fabry, Pompe, Etc.)

275.1 Wilson’s Disease E83.01

330.0 Leukodystrophy E75.29

330.1 Tay Sach’s Disease E75.02

Headache Disorders

307.81 Tension Headache G44.209

339.00 Cluster Headaches G44.009

346.00 Migraine Headache With Aura G43.109

ICD-9-CM to ICD-10-CM Codes for Neurology

Page 2: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

ICD-9 Code

DiagnosesICD-10Code

346.01Migraine With Aura, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.119

346.02Migraine With Aura, Without Mention Of Intractable Migraine With Status Migrainosus

G43.101

346.03Migraine With Aura, With Intractable Migraine, So Stated, With Status Migrainosus

G43.111

346.10 Common Migraine G43.009

346.11

Migraine Without Aura, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.019

346.12Migraine Without Aura, Without Mention Of Intractable Migraine With Status Migrainosus

G43.001

346.13Migraine Without Aura, With Intractable Migraine, So Stated, With Status Migrainosus

G43.011

346.20

Variants Of Migraine, Not Elsewhere Classified, Without Mention Of Intractable Migraine, Without Mention Of Status Migrainosus

G43.A0

346.20

Variants Of Migraine, Not Elsewhere Classified, Without Mention Of Intractable Migraine, Without Mention Of Status Migrainosus

G43.B0

346.20

Variants Of Migraine, Not Elsewhere Classified, Without Mention Of Intractable Migraine, Without Mention Of Status Migrainosus

G43.D0

346.21

Variants Of Migraine, Not Elsewhere Classified, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.A1

346.21

Variants Of Migraine, Not Elsewhere Classified, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.B1

346.21

Variants Of Migraine, Not Elsewhere Classified, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.C1

346.21

Variants Of Migraine, Not Elsewhere Classified, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.D1

346.30

Hemiplegic Migraine, Without Mention Of Intractable Migraine Without Mention Of Status Migrainosus

G43.409

ICD-9 Code

DiagnosesICD-10Code

346.31

Hemiplegic Migraine, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.419

346.32Hemiplegic Migraine, Without Mention Of Intractable Migraine With Status Migrainosus

G43.401

346.33Hemiplegic Migraine, With Intractable Migraine, So Stated, With Status Migrainosus

G43.411

346.40Menstrual Migraine, Without Mention Of Intractable Migraine Without Mention Of Status Migrainosus

G43.829

346.41Menstrual Migraine, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.839

346.42Menstrual Migraine, Without Mention Of Intractable Migraine With Status Migrainosus

G43.821

346.43Menstrual Migraine, With Intractable Migraine, So Stated, With Status Migrainosus

G43.831

346.50

Persistent Migraine Aura Without Cerebral Infarction, Without Mention Of Intractable Migraine Without Mention Of Status Migrainosus

G43.509

346.51

Persistent Migraine Aura Without Cerebral Infarction, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.519

346.52

Persistent Migraine Aura Without Cerebral Infarction, Without Mention Of Intractable Migraine With Status Migrainosus

G43.501

346.53

Persistent Migraine Aura Without Cerebral Infarction, With Intractable Migraine, So Stated, With Status Migrainosus

G43.511

346.60

Persistent Migraine Aura With Cerebral Infarction, Without Mention Of Intractable Migraine Without Mention Of Status Migrainosus

G43.609

346.61

Persistent Migraine Aura With Cerebral Infarction, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.619

346.62

Persistent Migraine Aura With Cerebral Infarction, Without Mention Of Intractable Migraine With Status Migrainosus

G43.601

346.63

Persistent Migraine Aura With Cerebral Infarction, With Intractable Migraine, So Stated, With Status Migrainosus

G43.611

ICD-9-CM to ICD-10-CM Codes for Neurology

Page 3: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

ICD-9 Code

DiagnosesICD-10Code

346.70

Chronic Migraine Without Aura, Without Mention Of Intractable Migraine Without Mention Of Status Migrainosus

G43.709

346.71

Chronic Migraine Without Aura, With Intractable Migraine, So Stated, Without Mention Of Status Migrainosus

G43.719

346.72Chronic Migraine Without Aura, Without Mention Of Intractable Migraine With Status Migrainosus

G43.701

346.73Chronic Migraine Without Aura, With Intractable Migraine, So Stated, With Status Migrainosus

G43.711

346.80 Ophthalmic Migraine G43.809

346.90 Migraine Headache, Unspecified G43.909

348.2 Idiopathic Intracranial Hypertension G93.2

784.0 Headache R51

784.0 Headache G44.1

784.40 Voice And Resonance Disorder, Unspecified R49.9

784.59 Other Speech Disturbance R47.02

Infections

322.9 Meningitis G03.9

323.9 Encephalitis G04.90

323.9 Myelitis G04.91

Injuries

852.20 Subdural Intracranial HematomaTraumatic Subdural Hemorrhage Without Loss Of Consciousness, Initial Encounter

S06.5X0A

Traumatic Subdural Hemorrhage Without Loss Of Consciousness, Subsequent Encounter

S06.5X0D

Traumatic Subdural Hemorrhage Without Loss Of Consciousness, Sequela

S06.5X0S

853.00 Traumatic Cerebral HemorrhageUnspecified focal traumatic brain injury without loss of consciousness, initial encounter

S06.300A

Unspecified Focal Traumatic Brain Injury Without Loss Of Consciousness, Subsequent Encounter

S06.300D

Unspecified Focal Traumatic Brain Injury Without Loss Of Consciousness, Sequela

S06.300S

ICD-9 Code

DiagnosesICD-10Code

854.00 Traumatic Brain InjuryUnspecified open wound of unspecified part of head, initial encounter

S06.9X0A

Unspecified Intracranial Injury Without Loss Of Consciousness, Subsequent Encounter

S06.9X0D

Unspecified Intracranial Injury Without Loss Of Consciousness, Sequela

S06.9X0S

854.10 Brain Injury With Intracranial WoundUnspecified open wound of unspecified part of head, initial encounter

S06.9X0A

Unspecified Intracranial Injury Without Loss Of Consciousness, Subsequent Encounter

S06.9X0D

Unspecified Intracranial Injury Without Loss Of Consciousness, Sequela

S06.9X0S

Intracranial And Spinal Tumors

191.6 Medulloblastoma C71.6

191.9 Glioma C71.9

192.2 Malignant Neoplasm Of Spinal Cord C72.0

194.3 Pituitary Cancer C75.1

225.2 Meningioma D32.9

237.5 Brain Tumor D49.6

237.70 Neurofibromatosis Q85.00

Motor Neuron Diseases

335.20 Amyotrophic Lateral Sclerosis G12.21

335.21 Progressive Muscular Atrophy G12.21

335.24 Primary Lateral Sclerosis G12.29

Movement And Cerebellar Disorders

307.20 Tic Disorder F95.9

307.23 Tourette’s Syndrome F95.2

332.0 Parkinson’s Disease G20

332.1 Secondary Parkinsonism G21.9

333.0 Progressive Supernuclear Palsy G23.1

333.1 Essential And Other Specified Forms Of Tremor G25.0

333.1 Essential And Other Specified Forms Of Tremor G25.1

333.1 Essential And Other Specified Forms Of Tremor G25.2

333.2 Myoclonus G25.3

Page 4: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

ICD-9 Code

DiagnosesICD-10Code

333.4 Huntington’s Disease G10

333.5 Hemiballismus G25.5

333.72 Acute Dystonia Due To Drugs G24.02

333.79 Acquired Torsion Dystonia G24.8

781.0 Spasms R25.2

781.0 Tremor R25.1

781.3 Ataxia R27.0

Muscular Dystrophies And Other Myopathies

359.0 Congenital Hereditary Muscular Dystrophy G71.2

359.1 Muscular Dystrophy G71.0

359.21 Myotonic Muscular Dystrophy G71.11

359.22 Myotonia Congenita G71.12

359.24 Drug-Induced Myotonia G71.14

359.3 Periodic Paralysis G72.3

359.4 Toxic Myopathy G72.2

359.6Symptomatic Inflammatory Myopathy In Diseases Classified Elsewhere

G73.7

359.71 Inclusion Body Myositis [IBM] G72.41

359.9 Myopathy, Unspecified G72.9

Other Neurological Disorders

324.1 Spinal Epidural Abscess G0.61

334.0 Friedreich’s Ataxia G11.1

334.1 Hereditary Spastic Paraplegia G11.4

336.1 Acute Infarction Of Spinal Cord G95.11

336.9 Myelopathy G95.9

336.9 Spinal Cord Compression G95.20

340 Multiple Sclerosis G35

341.0 Neuromyelitis Optica G36.0

342.90 Hemiplegia, Unspecified G81.90

343.9 Infantile Cerebral Palsy G80.9

741.90 Spina Bifida Q05.9

Peripheral Nervous System Disorders

335.10 Spinal Muscular Atrophy G12.9

350.10 Trigeminal Neuralgia G50.0

351.0 Bell’s Palsy G51.0

351.8 Hemifacial Spasms G51.8

356.1 Peroneal Muscular Atrophy G60.0

ICD-9 Code

DiagnosesICD-10Code

356.3 Refsum’s Disease G60.1

356.8 Other Specified Idiopathic Peripheral Neuropathy G60.8

356.9 Peripheral Neuropathy G60.9

357 Guillain-Barre Syndrome G61.0

358.00 Myasthenia Gravis G70.00

358.01 Myasthenia Gravis With Exacerbation G70.01

Seizure Disorders

345.00 Generalized Nonconvulsive Epilepsy W/O Mention Of Intractable Epilepsy G40.A01

345.00 Generalized Nonconvulsive Epilepsy W/O Mention Of Intractable Epilepsy G40.A09

345.01 Generalized Nonconvulsive Epilepsy W/Intractable Epilepsy G40.A11

345.01 Generalized Nonconvulsive Epilepsy W/Intractable Epilepsy G40.A19

345.10 Grand Mal Seizure G40.409

345.10 Myoclonic Seizures, Intractable G40.419

345.11 Generalized Convulsive Epilepsy With Intractable Epilepsy G40.311

345.11 Generalized Convulsive Epilepsy With Intractable Epilepsy G40.319

345.30 Grand Mal Status Epilepticus, Intractable G40.411

345.40 Complex Partial Seizures G40.209

345.40

Localization-Related (Focal) (Partial) Epilepsy And Epileptic Syndromes With Complex Partial Seizures, W/O Mention Of Intractable Epilepsy

G40.201

345.41

Localization-Related (Focal) (Partial) Epilepsy And Epileptic Syndromes With Complex Partial Seizures W/Intractable Epilepsy

G40.211

345.41

Localization-Related (Focal) (Partial) Epilepsy And Epileptic Syndromes With Complex Partial Seizures W/Intractable Epilepsy

G40.219

345.50 Simple Partial Seizures G40.109

345.51

Localization-Related (Focal) (Partial) Epilepsy And Epileptic Syndromes With Simple Partial Seizures W/Intractable Epilepsy

G40.111

345.51

Localization-Related (Focal) (Partial) Epilepsy And Epileptic Syndromes With Simple Partial Seizures W/Intractable Epilepsy

G40.119

345.60 Infantile Spasms W/O Mention Of Intractable Epilepsy G40.821

Page 5: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

ICD-9 Code

DiagnosesICD-10Code

345.60 Infantile Spasms W/O Mention Of Intractable Epilepsy G40.822

345.61 Infantile Spasms W/Intractable Epilepsy G40.823

345.61 Infantile Spasms W/Intractable Epilepsy G40.824

345.70 Epilepsy Partialis Continua W/O Mention Of Intractable Epilepsy G40.101

345.71 Epilepsy Partialis Continua W/Intractable Epilepsy G40.119

345.80Other Forms Of Epilepsy And Recurrent Seizures W/O Mention Of Intractable Epilepsy

G40.B01

345.80Other Forms Of Epilepsy And Recurrent Seizures W/O Mention Of Intractable Epilepsy

G40.B09

345.80Other Forms Of Epilepsy And Recurrent Seizures W/O Mention Of Intractable Epilepsy

G40.811

345.80Other Forms Of Epilepsy And Recurrent Seizures W/O Mention Of Intractable Epilepsy

G40.812

345.81Other Forms Of Epilepsy And Recurrent Seizures W/Intractable Epilepsy

G40.B11

345.81Other Forms Of Epilepsy And Recurrent Seizures W/Intractable Epilepsy

G40.B19

345.81Other Forms Of Epilepsy And Recurrent Seizures W/Intractable Epilepsy

G40.813

345.81Other Forms Of Epilepsy And Recurrent Seizures W/Intractable Epilepsy

G40.814

345.90 Epilepsy G40.909

345.91 Epilepsy, Unspecified With Intractable Epilepsy G40.911

345.91 Epilepsy, Unspecified With Intractable Epilepsy G40.919

779.0 Convulsions In Newborn P90

780.31 Febrile Seizures R56.00

780.32 Complex Febrile Seizure R56.01

780.33 Post-Traumatic Seizures R56.1

Sleep Disorders

327.20 Organic Sleep Apnea, Unspecified G47.30

327.21 Primary Central, Sleep Apnea G47.31

327.23 Obstructive Sleep Apnea (Adult) (Pediatric) G47.33

327.30 Circadian Rhythm Sleep Disorder G47.20

ICD-9 Code

DiagnosesICD-10Code

327.40 Organic Parasomnia G47.50

327.51 Periodic Limb Movement Disorders G47.61

333.94 Restless Legs Syndrome G25.81

347.00 Narcolepsy G47.419

347.01 Narcolepsy With Cataplexy G47.411

780.52 Insomnia G47.00

Miscellaneous

279.49 Autoimmune Disease, Not Elsewhere Classified D89.89

311 Depressive Disorder, Not Elsewhere Classified F32.9

331.83 Mild Cognitive Impairment, So Stated G31.84

331.9 Cerebral Degeneration, Unspecified G31.9

333.90 Unspecified Extrapyramidal Disease And Abnormal Movement Disorder G25.9

333.91 Stiff-Man Syndrome G25.82

334.8 Other Spinocerebellar Diseases G11.8

334.9 Unspecified Disorder Of Autonomic Nervous System G90.9

335.19 Other Spinal Muscular Atrophy G12.8

335.29 Other Motor Neuron Disease G12.29

341.9 Demyelinating Disease Of Central Nervous System, Unspecified G37.9

348.30 Encephalopathy, Unspecified G93.40

354.0 Carpal Tunnel Syndrome G56.00

355.9 Mononeuritis Of Unspecified Site G58.9

357.2 Polyneuropathy In Diabetes E11.42

357.3 Polyneuropathy In Malignant Disease G63

357.81 Chronic Inflammatory Demyelinating Polyneuritis G61.81

357.89 Other Inflammatory And Toxic Neuropathy G62.89

358.00 Myasthenia Gravis Without (Acute) Exacerbation G70.00

368.2 Diplopia H53.2

368.9 Unspecified Visual Disturbance H53.9

374.30 Ptosis Of Eyelid, Unspecified H02.409

377.10 Optic Atrophy, Unspecified H47.20

377.16 Hereditary Optic Atrophy H47.22

377.30 Optic Neuritis, Unspecified H46.9

386.11 Benign Paroxysmal Positional Vertigo H81.13

723.1 Cervicalgia M54.2

724.2 Lumbago M54.5

Page 6: ICD-9-CM to ICD-10-CM Codes for Neurology - Quest

This list is intended to assist ordering physicians in providing ICD-10 Diagnostics codes as required by Medicare and other Insurers. It includes some commonly found ICD-10 codes.

This list was compiled from the ICD-10-CM 2015 AMA manual. A current ICD-10-CM book should be used as a complete reference. The ultimate responsibility for correct coding belongs to the ordering physician.

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© 2015 Quest Diagnostics Incorporated. All rights reserved. MI4958 10/2015

Diagnostic Services

ICD-9 Code

DiagnosesICD-10Code

728.2 Muscular Wasting And Disuse Atrophy, Not Elsewhere Classified M62.50

728.85 Spasm Of Muscle M62.838

728.87 Muscle Weakness (Generalized) M62.81

729.1 Myalgia And Myositis, Unspecified M60.9; M79.1

729.2 Neuralgia, Neuritis, And Radiculitis, Unspecified

M79.2; M54.10

729.5 Pain In Limb M79.609

729.82 Cramp Of Limb R25.2

729.89 Other Musculoskeletal Symptoms Referable To Limbs R29.898

ICD-9 Code

DiagnosesICD-10Code

780.2 Syncope And Collapse R55

780.93 Retrograde Amnesia R41.2

781.2 Abnormality Of Gait R26.9

784.51 Dysarthria R47.1

787.20 Dysphagia, Unspecified R13.10

799.59 Other Signs And Symptoms Involving Cognition R41.89

V17.89 Family History Of Other Musculoskeletal Diseases Z82.69

V18.9 Family History Of Carrier Of Genetic Disease Z84.81

V5883 Encounter For Therapeutic Drug Monitoring Z51.81