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Page 1: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

RECOARCTATIA DE AORTACAZ CLINIC

NADIA ANGHELACHE, MARINELA SERBAN, MARIAN ALBU

INSTITUTUL DE BOLI CARDIOVASCULARE “PROF. DR. C.C. ILIESCU “INSTITUTUL CLINIC FUNDENI

Page 2: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

• Pacientul C.I., in varsta de 36 de ani, din mediul urban

• AHC: nesemnificative• APP: la varsta de 6 ani interventie

chirurgicala pentru coarctatie de aorta

Page 3: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

MOTIVELE INTERNARII

TAs = 200mmHg

TAs = 100mmHg

claudicatie intermitenta

Page 4: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

EXAMENUL OBIECTIV

• TA brat drept=200/90 mmHg• TA brat stang =190/90 mmHg• TAs membre inferioare = 100 mmHg• AV=96/minut regulat• Suflu sistolic gradul IV/VI in spatiul IV intercostal stang

parasternal , suflu sistolic gradul IV/VI interscapular• Puls palpabil la nivelul arterelor femurale bilateral si diminuat

distal bilateral

Page 5: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

ECG: ritm sinusal, 75/minut, axa QRS -15,HVS, modificarisecundare de repolarizare

Page 6: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Radiografia toracica

Page 7: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Ecocardiografia

• transtoracica: HVS ( SIV=19 ) Ao inel=19 Ao asc=28 Ao crosa=20valve aortice tricuspide

• transesofagiana:- pintene fibros ce proemina intraluminal la nivelul emergentei subclaviei, realizand un canal circulant de 3-4 mm

-gradient la nivelul aortei descendente80mmHg

Page 8: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Rezonanta magnetica nucleara

Page 9: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Aortografia

Page 10: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Tratament chirurgical

Rezectie + anastomozatermino-terminala

Rezectie + anastomozatermino-terminala extinsa

Incidenta crescuta a restenozei

Page 11: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Aortoplastie cu petec deDacron

Rezectie + interpozitie de graft

prostetic

Avantaj : incizia redusa a

peretelui aortic

Risc de anevrism

Indicatii:- coarctatie + anevrism

- recoarctatie

Risc de anevrism si infectii

Page 12: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Aortoplastia cu “ flap” artera subclavie

Avantaje: - tehnica operatorie simpla

-timp operator scurt

Dezavantaje: - sacrifica circulatia membrului sup. stang

- anevrism

- recoarctatie

Page 13: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Angioplastia cu balon

• De prima intentie in recoarctatia de aorta

• “ Balloon dilatation has largely been accepted as the treatment of choice for recoarctation of the aorta. “

Stent implantation for aortic coarctation and recoarctation

A.G. Magee Heart 1999

Page 14: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Angioplastia cu balon

• Rezultate bune 60-75% cazuri• Complicatii : - gradient rezidual transstenotic > =20 mmHg

in ~ 25 % din cazuri- restenozare- anevrism

• Implantarea de stent creste eficienta procedurii ( reduce gradientul presional transstenotic si riscul de anevrism )

Page 15: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Angioplastie cu balon

Pre-procedura Post-procedura

Page 16: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Angioplastie cu balon

Page 17: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

Gradientul sistolic transstenotic

Pre-angioplastie Post-angioplastie

Page 18: CAZ CLINIC NADIA ANGHELACHE, MARINELA · PDF filerecoarctatia de aorta caz clinic nadia anghelache, marinela serban, marian albu institutul de boli cardiovasculare “prof. dr. c.c

TAs=140mmHg

TAs=110mmHg

Claudicatie intermitenta

LA EXTERNARE