24
Pigment ed Villous Nodular Synovit

Pigment villos nodular Synovitis PVNS

  • Upload
    -

  • View
    285

  • Download
    0

Embed Size (px)

Citation preview

Page 1: Pigment villos nodular Synovitis PVNS

Pigmented

Villous

Nodular

Synovitis

Page 2: Pigment villos nodular Synovitis PVNS

• 基本資料 :32 歲男性,勞力工作• 兩個月前,左腳腫痛,走路走不遠,後來疼痛加劇• 一個月前,左後膝窩處出現一個軟軟的腫瘤

Page 3: Pigment villos nodular Synovitis PVNS

• 腫瘤變的更大病患至醫院就診• Doctor: 為一個貝克式囊腫• 建議手術 !• 病人接受手術………… 但是 B

Page 4: Pigment villos nodular Synovitis PVNS

• 切除術開了 七個小時 • 醫生後來說不是囊腫…• 那切下來的東西是什麼 ??病人 : 醫生說再看看 ?

Page 5: Pigment villos nodular Synovitis PVNS

膝蓋週圍常見的囊腫

Page 6: Pigment villos nodular Synovitis PVNS

Synovial cysts• herniation of

synovial tissue into the surrounding soft tissue

• 有時連接的通道消失了和其他的Ganglion/Bursa不易區分

S

Page 7: Pigment villos nodular Synovitis PVNS

Popliteal (Baker‘s) cyst• 膝蓋最常見的腫瘤• Communication

posterior joint capsule /gastrocnemius-semimembranosus recess. • "ball-valve” • knee flexion/open

extension/close

S

Page 8: Pigment villos nodular Synovitis PVNS

• 大部分沒有症狀,但是如果太大,會造成神經,血管的壓迫大部分發生於屈曲時• 有時囊腫會破裂,會造成膝窩的腫脹,靜脈栓塞和週圍組織的血腫

Page 9: Pigment villos nodular Synovitis PVNS

有時會有骨頭漂至囊腫內

Page 10: Pigment villos nodular Synovitis PVNS

• 最近……膝後的腫瘤更大,整個膝蓋腫無法彎曲• PE: ROM 0~30

Severe swelling and tenderness , soft tissue mass over operation scar .

• PVNSMRI ??

Page 11: Pigment villos nodular Synovitis PVNS

T1 Saggital

P F

QF muscle

Soft tissuetumor

Page 12: Pigment villos nodular Synovitis PVNS

Soft tissuetumor

Soft tissue cyst

Page 13: Pigment villos nodular Synovitis PVNS

MRI 報告 :PVNSExcision biopsy

Posterior

順原傷口Anterior

`

Arthroscope ?Open arthrotomyOpen arthrotomy

Page 14: Pigment villos nodular Synovitis PVNS

AnteriorOpen Arthrotomy

Page 15: Pigment villos nodular Synovitis PVNS

AnteriorOpen Arthrotomy

ACL*

Page 16: Pigment villos nodular Synovitis PVNS

*

PosteriorOpen Arthrotomy

Page 17: Pigment villos nodular Synovitis PVNS

• 病理報告 :• Anterior: PMN,

lymphoid follicles,

Hemosiderin PVNS• Posterior: Bursitis with inflammation

Page 18: Pigment villos nodular Synovitis PVNS

PVNSRecurrent

hemoarthrosisBenign disease with

malignant behaviorEasily local

recurrence• High recurrence

rate• Long recurrence

period

Page 19: Pigment villos nodular Synovitis PVNS

• 正常關節 / 肌腱的滑膜會不斷的增生• 關節腔會發炎,增厚• 組 織 內 含

Hemosiderin外觀看起來暗紅色• 形成絨毛 (Villous)或結節狀 (Nodular)

Pigmented

Villous

Nodular

Synovitis

Page 20: Pigment villos nodular Synovitis PVNS
Page 21: Pigment villos nodular Synovitis PVNS
Page 22: Pigment villos nodular Synovitis PVNS

• Etiology --- unknown• Location

– Monarticular: Knee (75%)> Hip > Wrist > Ankle > Shoulder

– Polyarticular 少見• 臨床症狀 : 痛,活動受限,腫脹

Page 23: Pigment villos nodular Synovitis PVNS

• Diffuse type Large joint

Localized type Small joint • 診斷 關節抽吸 :Sero-sanguineou

“Without” trauma history• MRI

• T2 image: hemosiderin depositionLow signal

Page 24: Pigment villos nodular Synovitis PVNS

• 好發於 20~50 歲年輕人• Non-surgical Treatment

– Intra-articular injection• Steroid • Yttrium-90 silicate (RA,

knee)– Radiation therapy

• Post-op. (35 Gy / 15 fractions)

• 術後行放療證實可以減少復發