08.ELBABA M.A. Answers SAT8 for MRCPCH,2009.pdf

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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    3 July 2009

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    SAT FOR

    MRCPCH

    Part 1&2Series #Series #Series #Series # 8888Question number: Total is 10 cases

    Question Format: Best of many & Extended match

    Time allowed: 20 MinutesTotal Marks: 20

    Set your time & write in the answer sheet

    Answer is available on request & your score is confidential

    Please, do not turn this page until you asked to start

    Visit MRCPCH 2009 Website for all educational materials

    http://sites.google.com/site/mrcpch2009/

    http://sites.google.com/site/mrcpch2009/http://sites.google.com/site/mrcpch2009/http://sites.google.com/site/mrcpch2009/
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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    3 July 2009

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    Self-Assessment Test for MRCPCH / Series # 8

    Case # 1 (2 marks)12 years old girl is admitted to the hospital with burns on her legs which she

    obtained while playing near a bonfire. The burn was treated and starts to heal.While in hospital, it was noted that her behavior was odd. Her concentration span

    was very poor. She was suddenly changing her attention from one conversation and

    shouts something to another patient. On one occasion, she had been walking a little

    unsteady across the ward when she fell for no apparent reason. Another time she

    had fallen out of bed. Apart from parents divorce at age of 18 months, there was

    nothing significant in family or social history. For the last few months her behavior

    had been unpredictable and in view of this she had been sent to stay with an aunt

    for some weeks during the holiday. Since that time, the teachers in school had been

    observed deterioration in her performance. There was a past history of

    tonsillectomy at age of 6 years and the usual childhood infections as coryza, measles

    and recently chicken pox. Her cranial nerves and fundus exam are intact. She hadsudden grimaces and jerky movements of her arms, and occasional abnormal

    posture of her limbs. Her gait is unsteady. There was an increased tone and reflexes

    mainly over both lower limbs with positive planter reflexes. Rombergs test couldnt

    be done. Her FBC, ESR and skull X-ray are within normal.

    1. What is the most likely diagnosis? (Select ONE answer only)A. Drug poisoningB. SLEC. HyperthyroidismD. ChoreaE. Conduct disorderF. SchizophreniaG. Anxiety neurosisH. Hepatic encephalopathyI. Uremic syndromeJ. Subacute sclerosing panencepalitisK. Psychomotor epilepsyL. Myoclonic epilepsyM.Frontal lobe tumorN. Lundau Kleffner syndromeO. Rett syndromeP. AutismQ. Chronic fatigue syndromeR. EncephalitisS. Cow mad diseaseT. Alzheimer diseaseU. DementiaV. Vitamin B12 deficiencyW.Vitamin B6 deficency

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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    Case # 2 (4 marks)18 hours ago a pregnant lady had delivered a 36 weeks old girl weighting 2.650 kg.

    She was completely healthy woman with appropriate antenatal care. The baby is

    healthy as well and didnt require any resuscitation post delivery and started breast

    feeding with good suction. Apart from abnormally looked genitalia the baby is

    normal by quick inspection. This is the second child for this mother; her first sonhad died at the age of 2 weeks secondary to sever gastroenteritis and dehydration.

    1. What is the initial action you do now? (Select TWO answers only)A. Stop breast feedingB. Give IV Saline bolusC. Check blood glucoseD. Consult the parents to avoid giving a name now.E. Check serum electrolytesF. Complete you clinical examinationG. Urgent pelvic ultrasoundH. Buccal smearI. Talk to obstetricianJ. Check cord blood gasK. Check the placenta and umbilical cord

    2. What are the most two important signs helping in diagnosis? (Select TWO

    answer only)A. OFCB. Blood pressureC. Feeling the testisD. Dehydration statusE. HypopigmentationF.

    Urine volumeG. Patent anus

    H. Sacral agenesisI. TempratureJ. Eye examinationK. Primative reflexesL. Abnormal earM.Palpable kidneyN. Bulging fontanelsO. Dysmorphic faceP. PolydactylyQ.

    Cardiac murmurR. Hand anomaly

    S. Cleft palateT. LethargyU. Urine specific gravityV. Palpable bladderW.HepatomegalyX. Height

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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    Case # 3,4,5 & 6 (Extended Match) ( 2 mark for each, total 8)Choose the one most likely diagnosis from the list below which best matches each of thefollowing cases.Note:Each option may be used once, more than once or not at all.

    SELECT ONE ANSWER ONLY FOR EACH QUESTION

    3. 5 weeks newborn presented to OPD with difficulty in feeding, sweating andpoor weight gain. Baby is full term with uneventful pregnancy and delivery.

    The baby had discharged on second day of life completely healthy. On

    examination he has, mild tachypnea 50/m, tachycardia 180 b/m, normal

    temp. & blood pressure. Lungs are clear and normal cardiac examination.

    Chest X-ray shows only mild cardiomegaly, ECG is normal. G

    4. 5 weeks newborn presented to OPD with difficulty in feeding, sweating and

    poor weight gain. Baby is full term with uneventful pregnancy and delivery.

    The baby had discharged on second day of life completely healthy. On

    examination he has, mild tachypnea 50/m, tachycardia 180 b/m, normal

    temp. & blood pressure. Lungs are clear and normal cardiac examination.

    Chest X-ray shows only mild cardiomegaly, ECG shows only deep Q wave. F5. 5 weeks newborn presented to OPD with difficulty in feeding, sweating and

    poor weight gain. Baby is full term with uneventful pregnancy and delivery.

    The baby had discharged on second day of life completely healthy. The baby

    has Flu for the last 3 days. On examination he has, mild tachypnea 50/m,

    tachycardia 180 b/m, and normal temp. & blood pressure. Lungs show

    bilateral crackles and normal cardiac examination. Chest X-ray shows

    moderate cardiomegaly, ECG shows biventricular enlargement. I

    6. 5 weeks newborn presented to OPD with difficulty in feeding, sweating and

    poor weight gain. Baby is full term with uneventful pregnancy and delivery.

    The baby had discharged on second day of life completely healthy with soft

    systolic murmur. On examination he has, mild tachypnea 50/m, tachycardia180 b/m, and normal temp. & blood pressure. Lungs show bilateral crackles.

    There was a systolic murmur and loud 2nd

    sound on cardiac examination.

    Chest X-ray shows moderate cardiomegaly, ECG shows biventricular

    enlargement. B

    Select your answers from the following list:A. Small VSDB. Large VSDC. Aortic stenosisD. Coarctation of the AortaE.

    Total anomalous pulmonary venous drainageF. Anomalous left coronary artery

    G. Arterio-venous malformationH. Ebstein anomalyI. MyocarditisJ. PericarditisK. Protein C deficiencyL. Suprventricular tachycardia

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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    Case # 7 (2 marks)10-year-old girl presented with a history of progressive loss of vision and painful

    eyes. She has an area of numbness over her left side of the face. She is fully

    conscious but has developed progressive ataxia over the last few weeks. She is a

    completely healthy girl before that and achieving well in school until this year.

    Pregnancy and delivery were uneventful. Brain MRI shows scattered areas ofdemyelination in white matter over both hemispheres.

    1. What is the main lines of treatment? (Select TWO answers only)A. ReassuranceB. Behavioral therapyC. IV AntibioticsD. IV AcyclovirE. SteroidF. IVIGG. PlasmaphoresisH. CarbamazepineI. InterferonJ. Bone marrow transplantationK. HaloperidolL. NSAIDsM.PyridoxineN. BiotinO. ThiamineP. Refer to PsychiatristQ. RadiotherapyR. Immunosupprion

    Case # 8 (1 marks)Alex is 14 years old girl. Currently she is inpatient for the last 4 days following an

    appendicectomy. She is otherwise fit and well. You have just finished the ward

    round, during which said that she could be discharged. Alex has asked to speak to

    you alone before she goes home. She want you to prescribe an oral contraceptive

    pills for her.

    1. What is your response and action? (Select ONE answer only)

    A. I will tell her parents to take the appropriate actionB. I will prescribe that without any problem to avoid teenage pregnancyC. I will prescribe for her the pills after checking her competenceD. I will advice her to avoid discussing this matter with her parentsE. I will refuse that and will not prescribe anything like thatF. I will not warn her about sexually transmitted diseasesG. I will prescribe that according to the background social circumstancesH. I will call my senior and nurses to discuss with herI. I will contact the social worker to be involved in her managementJ. I will advice her to bring the partner for counselingK. I will recommend the mechanical barrier which is more protective

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    SAT for MRCPCH Part 1& 2 ELBABA M.A.ELBABA M.A.ELBABA M.A.ELBABA M.A.

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    Case # 9 (2 marks)6 years old boy had a past history of medulloblastoma. It was operated 4 years ago.

    He is presented to you clinic with the following result of Insulin stimulation test:

    Time / min 0 20 30 60 90 120

    Glucose (mmol/l) 4.5 1.8 1.6 6.3 7.5 8.1

    Cortisol (nmol/l) 507 - 581 992 741 582GH (mU/l) 0.9 - 0.7 1.7 4.2 4.6

    TSH (mU/l) 41 > 60 - > 60 - -

    FSH (u/l) 1.6 > 30 - > 30 - -

    LH (u/l) 1.2 2.8 - 3.2 - -

    1. What does the test show? (Select ONE answer only)

    A.Normal test resultB. Growth hormone deficiencyC. PanhypopituitarismD. Primary hypothyroidismE. Secondery hypothyroidismF. Isolated hyperthyroidismG. Isolated deficiency of cortisolH. GnRH deficiencyI. GnRH excessJ. Both B & DK. Both E & GL. All B,D & HM.All B, E, G & H

    Case # 10 (1 marks)A baby born at 28 weeks gestation is now 3 months old with chronic lung disease.

    He is on nasal cannula Oxygen at home. 2 days ago he developed cough and

    respiratory distress with increasing Oxygen requirement. You have asked for

    arterial blood gas which shows the result below:PH 7.20

    PO2 11.2 kPa

    PCO2 13 kPaHCO3 28 kPaBe +9.3

    1. How do you interpret this result (Select ONE answer only)

    A. Respiratory acidosisB. Metabolic acidosisC. Compensated Metabolic acidosisD. Compensated Respiratory acidosisE. Partially Compensated Respiratory acidosisF. Partially Compensated Metabolic acidosisG.Normal gas for chronic lung disease child

    End of the testELBABA M.ELBABA M.ELBABA M.ELBABA M.A.A.A.A.