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Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi

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Page 1: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 2: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 3: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 4: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 5: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 6: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 7: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 8: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 9: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
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Page 16: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 17: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 18: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 19: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 20: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi
Page 21: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi

Answer• 1.Alder- reilly anamoly.• 2. plasma cells• 3. Burkett lymphoma “starlight”• 4. Chediak-Steinbrinck –Higashi Anomaly• 5. Reed sternberg cells- Hogdkin lymphoma• 6. Smudge cells –CLL/SLL• 7. ALL• 8. AML• 9. May-Hegglin Anomaly, associated with giant platelets• 10. hairy Cell lymphoma-B cell• 11. Sezary- t cell• 12. Dsyelomyeloiesis• 13. Pelger-Huet Bodies• 14. Nuclear extrusion anomaly• 15. Dohle bodies• 16.Promyelocyte• 17. Band• 18. Myelocyte• 19.metamyelocyte• 20. Auer rods

Page 22: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi

Alder-Reilly Anomaly1.Cytoplasmic inherited

abnormalities of neutrophils.

2. Seen in inheritedHunter’s or Hurler’s syndromes.3. Heavy granulation.4. Also seen in mucopolysaccharide storage disease.5. Caused by an inherited autosomal recessive trait.

Page 23: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi

May-Hegglin Anomaly

1. Rare, autosomal dominant, qualitative leukocyte abnormality.

2. Appears as Dohle-like inclusions.

3. Associated with giant platelets , thrombocytopenia , and slight bleeding tendency.

4. Cytoplasmic inclusions in May-Hegglin anomaly are PAS negative.

5. Inclusion found in eosinophils, basophils, monocytes, and neutrophils.

6. Cytoplasmic inclusions results from structural RNA.

Page 24: Answer 1.Alder- reilly anamoly. 2. plasma cells 3. Burkett lymphoma “starlight” 4. Chediak-Steinbrinck –Higashi

Chediak-Steinbrinck –Higashi Anomaly

1. Rare, autosomal recessive disorder that results in qualitative abnormalities in all types of leucocytes.

2. Giant , coarse , irregular , peroxidase positive lysosome granules are found in the cytoplasm of granulocytes and monocytes.

3. Patients demonstrate abnormal pigmentation ,pancytopenia, neuropathies, and recurrent infections.