BLOUNT’S DISEASE

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    BLOUNTS DISEASE

    Disusun Oleh :

    DODDY TISNA

    Pembimbing :Dr. Giri Marsela, Sp.OT

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    PENDAHULUAN

    Tibia vara dapat terjadi pada setiap kelompok umur

    pada anak yang sedang diklasifikasikan sebagai

    infantil (1-3 tahun), juvenil (4-10 tahun), dan remaja

    (11 tahun atau lebih tua). Prevalensi Bentuk kekanak-kanakan lebih sering

    terjadi pada anak perempuan. Bentuk remaja atau

    remaja lebih sering terjadi pada anak laki-laki.

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    PENDAHULUAN

    Kelainan ini lebih sering terjadi pada anak-anak

    Amerika Afrika dibandingkan dengan ras lain.

    Faktor Risiko untuk penyakit blount, antara lain :

    Afrika Amerika etnis, Kegemukan dan Usia diniberjalan. Varus lebih besar pada tibial dari sisi

    femoralis adalah faktor risiko untuk penyakit Blount

    kekanak-kanakan dan remaja.

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    DEFENISI

    Tibia vara idiopatik atau penyakit Blount

    adalah gangguan yang jarang terjadi yang

    ditandai oleh kelainan pertumbuhan sisi media

    epifisis tibia proksimal, mengakibatkan

    angulasi varus progresif di bawah lutut.

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    ETIOLOGI

    Penyakit blount terjadi pada anak-anak dan remaja.

    Penyebab penyakit ini belum diketahui, tetapi

    diperkirakan karena efek dari kelainan pada lempeng

    pertumbuhan. Pada komponen bagian dalam tibia tepatnya di bawah

    lutut terjadi kegagalan untuk berkembang secara

    normal oleh karena adanya angulasi dari tulang.

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    ETIOLOGI

    Seperti pada bowleg, yang mana cenderung

    ditujukan pada perkembangan anak-anak.

    Penyakit blount bersifat progresif dan kondisi ini

    buruk. Hal ini dapat dikarenakan pembengkokan yang

    berat dari kaki dan dapat terjadi pada satu atau

    kedua kaki.

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    ETIOLOGI

    Kondisi seperti ini lebih sering didapati pada

    anak-anak keturunan afrika.

    Penyakit blount juga dihubungkan dengan suatu

    kegemukan, orang-orang pendek dan berjalanbelum saatnya. Penyakit ini tidak bisa

    dihubungkan secara jelas dari faktor genetik.

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    KLASIFIKASI DAN STAGING

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    MANIFESTASI KLINIK

    tonjolan metafisis media hebat,

    torsi tibia interna,

    ketidaksesuaian panjang kaki,

    deformitas genu varum progresif lambat, dan

    nyeri

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    DIAGNOSA

    Anamnesa yang lengkap

    Pemeriksaan fisik

    Pemeriksaan Laboratorium

    Pemeriksaan radiologi

    Foto Rontgen tibia

    CT-Scan

    MRI

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    DIAGNOSA BANDING

    Membungkuk fisiologis kaki

    Hypophosphatemic rakhitis

    Trauma plat metaphysis atau pertumbuhan

    Osteochondroma

    Metaphyseal chondrodysplasia

    Focal fibrocartilaginous dysplasia

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    KOMPLIKASI

    Kambuhnya deformitas mengarah ke

    ekstremitas keselarasan abnormal dan arthritis

    degeneratif.

    Limb-panjang bisa mengakibatkan ketimpangan.komplikasi Postosteotomy termasuk komplikasi

    neurovaskular dan sindrom kompartemen.

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    PROGNOSA

    Karena tingkat kekambuhan lebih tinggi pada

    pasien dirawat setelah 4 tahun (70-75%)

    dibandingkan pada pasien yang diobati sebelum

    usia 4 (20-30%), osteotomy dini (sebelum usia4) boleh dilakukan jika bracing tidak berhasil.

    Pasien dengan pengobatan terlambat atau

    pengobatan tidak lengkap memiliki peningkatan

    risiko radang sendi lutut.

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    PENATALAKSANAAN

    Anjuran diet harian

    Anjuran aktifitas fisik harian

    Farmakoterapi

    Melakukan tindakan umum

    Operasi

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    DAFTAR RUJUKAN

    http://www.patient.co.uk/doctor/Blount%27s-

    Disease.htm

    http://en.wikipedia.org/wiki/Blount%27s_disease

    http://indonesian.orthopaedicclinic.com.sg/?p=900

    http://medicalcom.wordpress.com/2011/04/21/tibia-

    vara/

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    http://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://en.wikipedia.org/wiki/Blount%27s_diseasehttp://indonesian.orthopaedicclinic.com.sg/?p=900http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://indonesian.orthopaedicclinic.com.sg/?p=900http://en.wikipedia.org/wiki/Blount%27s_diseasehttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htm
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    DAFTAR RUJUKAN

    ^ Clarke SE, McCarthy JJ, Davidson RS (March 2009). "Treatment of Blount

    disease: a comparison between the multiaxial correction system and other external

    fixators".J Pediatr Orthop29 (2): 1039. doi:10.1097/BPO.0b013e3181982a62.

    PMID19352232. http://meta.wkhealth.com/pt/pt-core/template-

    journal/lwwgateway/media/landingpage.htm?issn=0271-

    6798&volume=29&issue=2&spage=103. ^synd/1470 at Who Named It?

    ^ W. P. Blount. Tibia vara: osteochondrosis deformans tibiae. Journal of Bone and

    Joint Surgery, Boston, 1937, 19: 1-29.

    ^ McCarthy JJ, MacIntyre NR, Hooks B, Davidson RS (March 2009). "Double

    osteotomy for the treatment of severe Blount disease".J Pediatr Orthop29 (2):

    1159. doi:10.1097/BPO.0b013e3181982512. PMID19352234.

    http://meta.wkhealth.com/pt/pt-core/template-

    journal/lwwgateway/media/landingpage.htm?issn=0271-

    6798&volume=29&issue=2&spage=115.

    7/15/2013 BLOUNT'S DISEASE, RSPHM 23

    http://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Digital_object_identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982a62http://en.wikipedia.org/wiki/PubMed_Identifierhttp://www.ncbi.nlm.nih.gov/pubmed/19352232http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Blount's_diseasehttp://www.whonamedit.com/synd.cfm/1470.htmlhttp://en.wikipedia.org/wiki/Who_Named_It?http://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://en.wikipedia.org/wiki/Digital_object_identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982512http://en.wikipedia.org/wiki/PubMed_Identifierhttp://www.ncbi.nlm.nih.gov/pubmed/19352234http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://www.ncbi.nlm.nih.gov/pubmed/19352234http://en.wikipedia.org/wiki/PubMed_Identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982512http://en.wikipedia.org/wiki/Digital_object_identifierhttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Who_Named_It?http://www.whonamedit.com/synd.cfm/1470.htmlhttp://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://www.ncbi.nlm.nih.gov/pubmed/19352232http://en.wikipedia.org/wiki/PubMed_Identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982a62http://en.wikipedia.org/wiki/Digital_object_identifierhttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Blount's_disease
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    TERIMA KASIH

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