T HE PIERRE ROBIN syndrome13 is charactenized

by three defects : micrognathia,cleft palate and glossoptosis. It is adistinct clinical entity possessing a historythat is almost monotonous in regularity,and with physical findings so striking as tonot easily be overlooked. Definitive formsof therapy are available and with propermanagement a good prognosis can be givenin the majority of cases. The syndrome iswell documented in the French litenatureıbut has gained little recognition in theUnited States. After encountering a 2-month-old white male with Pierre Robinsyndrome and severe bilateral congenitalglaucoma, our attention was directed toocular involvement in these cases. Foursuch patients with bilateral ocular diseasewere subsequently reported.