Tugas Baca Displacement of the Lens

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    ECTOPIA LENTISRAMA

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    !

    Displacement of the lens from its normal position

    (in patellar fossa) results from partial or complete

    rupture of the lens zonules.

    Positioned just posterior to the iris and is

    supported by zonular fibers arising from the

    ciliary body.

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    CLINICO-

    ETIOLOGICAL

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    Clinico-Etiological Types

    Ectopia Lentis

    Hereditary

    w/ Systemic

    w/o Systemic

    Acquired

    Traumatic

    Consecutive/Spontaneous

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    Without Systemic

    AssociationsFamilial Ectopia LentisBilaterally symmetrical

    superotemporal

    AD fashion

    Ectopia lentis et pupillae

    Pupil and lens in opposite

    directions

    Small, slit-like, and dilate-poorly

    pupil

    Aniridia

    Absence of iris

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    With Systemic Associations

    Marfan Syndrome

    AD

    Bilaterally symmetrical

    superotemporal subluxation (80%)

    Dislocation into anterior chamber or

    vitreous (20%)

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    With Systemic Associations

    Homocystinuria:

    AR, inborn error of metabolism

    Inferonasal

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    Traumatic displacement of the

    lensAssociated with concussion injuries.Couchingis an iatrogenic posterior dislocation of

    lens performed as a treatment of cataract in

    olden days.

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    Consecutive or spontaneous

    displacement

    Intraocular diseases giving rise to mechanical

    stretching, inflammatory disintegration or

    degeneration of the zonules.

    Hypermature cataract, buphthalmos, highmyopia, staphyloma, intraocular tumours and

    uveitis.

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    TOPOGRAPHICAL

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    Subluxation

    Partial displacement in which lens is moved

    sideways (up, down, medially or laterally), but

    remains behind the pupil.

    Partial rupture or unequal stretching of thezonules.

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    Subluxation

    Clinical Features

    Defective vision

    Uniocular diplopia

    Anterior Chamberdeep and irregular

    Iridodonesis

    Dark Edge

    Complications

    Refractive error

    Complete dislocation

    Cataractous changesUveitis

    Secondary glaucoma

    Management

    Spectacles/contactlenses

    Surgery

    Lensectomy with

    anterior vitrectomy

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    LuxationAll the zonules are severed from the lens.

    A dislocated lens may be incarcerated into the

    pupil or present in the anterior chamber, the

    vitreous (where it may be floating lens nutans;

    or fixed to retina

    lens fixata), sub-retinal space,subscleral space or extruded out of the globe,

    partially or completely.

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    LuxationClinical Features

    Posterior: deep anterior

    chamber, aphakia in

    pupillary area, and

    iridodonesis.Ophtalmoscopic

    examination reveals lens

    in the vitreous cavity.

    Anterior: deep anteriorchamber and presence of

    lens in the anterior

    chamber.

    Clear lens looks like an oil

    drop in the aqueous.

    Complications

    Uveitis

    Secondary glaucoma

    ManagementAnterior: ASAP!

    Posterior: if only

    causing uveitis or

    uncontrolledglaucoma

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    Khurana, Comprehensive Ophtalmology 4th Edition (Step by Step)

    Vaughn and Asburys, General Ophtalmology 17th Edition

    Kanski, Clinical Ophtalmology

    DANK U WEL