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㸰㸳ᅇᕝᓮᅜㄪᰝᡂ⦼ ≉ᐃ㠀Ⴀάἲே ᪥ᮏᕝᓮ◊✲ ᕝᓮᅜㄪᰝᢸᙜ 㹙㐃⤡ඛ㹛 329-0498 ᰣᮌ┴ୗ㔝ᕷ⸆ᖌᑎ 3311-1 ⮬་⛉Ꮫබ⾗⾨⏕ᏛᩍᐊẼ ᕝᓮᅜᏛㄪᰝᒁ 㐃⤡ᢸᙜ ᑠబぢගᶞᒇ௦┿ᘪ∾㔝ఙᏊ୰ᮧዲ 7(/ 0285-44-6192 )$; 0285-44-7217 2019 9

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Page 1: 1* B)¼ - Jichi · 2019-09-25 · 1* c+¬ &É ± Û+« Ë%Ê'2'¼ Ô#. B $ ( b 1 Z K S>&2018 º10 v9 ¥ +« ±18-070 >' 2.0[ ¨ 2.1. H* X í*/ H"á b º N&ã 4# d24 G b ² \1* [ Ì

329-0498 3311-1

0285-44-61920285-44-7217

2019 9

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-1-

25

1970 2 1 24 1-43

2017 2018 2 25

IG IGIG IG

25 1

1.

25 100100 2017 1 1 2018 12 31 2

241,816

http://www.kawasaki-disease.net/kawasakidata/

2018 10 918-070

2.

2.1.24 2018 12 31

395,238 228,107 167,131 2017 20182017 15,164 8,635 6,529 2018 17,364 9,964 7,400

0-4 10 2017 313.6 348.9 276.5 2018 359.1 402.6313.4 2018 2015 330.2

2.2.

2015 9-10 20151 2016 6-710-11 2016 1

2.3.25 3,785

2,424 2,276 126131 151

Page 3: 1* B)¼ - Jichi · 2019-09-25 · 1* c+¬ &É ± Û+« Ë%Ê'2'¼ Ô#. B $ ( b 1 Z K S>&2018 º10 v9 ¥ +« ±18-070 >' 2.0[ ¨ 2.1. H* X í*/ H"á b º N&ã 4# d24 G b ² \1* [ Ì

-2-

2017 422.2 388.9 385.72018 495.7 436.0 434.62017 134.9 166.7 187 2018 158.1 202.4

252.2 2017 2018

2.4.25,661 78.9% 565 1.7% 6,289

19.3%

2.5.1,604 4.9% 1,042 5.6% 562 4.0%

11 0.03% 117 0.36%1,248 3.84% 2 0.01% 0 0% 283 0.87%

2,901 8.9% 1,850 9.9% 1,051 7.5%35 0.11% 309 0.95%

2,120 6.52% 6 0.02% 4 0.01% 503 1.55%

845 2.6% 548 2.9% 297 2.1%36 0.11% 206 0.63% 488

1.50% 6 0.02% 1 0.003% 164 0.50%

2.6.IG 30,784 94.6% IG 6,06119.7% IG 4,076 13.2%

IG 30,042 97.7% IG 11900-2099mg/kg 29,443 95.7% 900-1099mg/kg

754 2.45% 1 30,141 98.0% 2 5961.94% IG 5 10,710 34.8%

2.7.1 14,156 43.5%

8,465 3,187 758

2.8.696 2.1% 386 2.1% 310 2.2%

419 1.3%

214 51.1% 199 47.5%

3.

3.1.1,816 12 1,804

1,357 75.2Excel 139

27

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-3-

1,357 924 68.165.2 95.5

3.2.1

24 2018 12 31 395,238228,107 167,131 2017 2018 2017

15,164 8,635 6,529 2018 17,364 9,964 7,400

2 2,8741 1,900

944956

20-4 10 2017 313.6 348.9 276.5 2018 359.1 402.6

313.4 2018 2015 330.2

2018 / 1.35 1.28

1 1979 1982 1986 31995 2010 12,000

1986 3 2012 1979 12 2013 15,000 1982 2

2016 2017 2018

2 2018 359.1402.6 313.4

3.3.3

2015 9-102015 1 2016 6-7

10-11 2016 12015 2016 1

2013 2018 2 94

3.4.25 2017 2018 2 25

4 71% 109-11 2017 472.2 2018 502.2

24 9-11 24 255

Page 5: 1* B)¼ - Jichi · 2019-09-25 · 1* c+¬ &É ± Û+« Ë%Ê'2'¼ Ô#. B $ ( b 1 Z K S>&2018 º10 v9 ¥ +« ±18-070 >' 2.0[ ¨ 2.1. H* X í*/ H"á b º N&ã 4# d24 G b ² \1* [ Ì

-4-

3.5.0-4 10 3 25

3,7852,424 2,276 126

131 1512017 422.2 388.9 385.7

2018 495.7 436.0 434.62017 134.9 166.7 187 2018 158.1 202.4

252.22017 2018

6 2015 20182018

3.6.25,661 78.9% 565 1.7% 6,289

19.3% 4 4 4,45970.9% 3 23.4% 2 5.1 %

5A 5 2002 2

17 5 65 B 4

3.7.1,478 4.5% 868 4.7% 610 4.4%

1

3.8.2017 2018 6 3 3 6 9

2 1 31 6

3.9.1 1

31,604 4.9% 1,042 5.6% 562 4.0%

11 0.03% 117 0.36%1,248 3.84% 2 0.01% 0 0% 283 0.87%

22,901 8.9% 1,850 9.9% 1,051 7.5%

35 0.11% 309 0.95%2,120 6.52% 6 0.02% 4 0.01% 503 1.55%

2845 2.6% 548 2.9% 297 2.1%

36 0.11% 206 0.63% 488 1.50%6 0.02% 1 0.003% 164 0.50%

Page 6: 1* B)¼ - Jichi · 2019-09-25 · 1* c+¬ &É ± Û+« Ë%Ê'2'¼ Ô#. B $ ( b 1 Z K S>&2018 º10 v9 ¥ +« ±18-070 >' 2.0[ ¨ 2.1. H* X í*/ H"á b º N&ã 4# d24 G b ² \1* [ Ì

-5-

2

3.52.6

27

U 715 1997-1998 20.1%

8

3.10.4 8,192 25.2% 20,679 63.6% 4

2 2 2 67.8% 42 60.3%

IG 5 10,710 34.8% 2 22 75.4% 5 2 67.4%

2 IG 8

3.11.IG 30,784 94.6% 17,608 94.7% 13,17694.6% 9 IG 6,061 19.7%

10IG 4,076 13.2%

3,463 13.8% 6712.7% 546 10.4%

699 17.1%3,447 84.6% 1

1011

IG 30,042 97.7%12 IG 1 1900-2099mg/kg

29,443 95.7% 900-1099mg/kg 754 2.45% 130,141 98.0% 2 596 1.94% 13 IG 1

1900-2099mg/kg 97.1%2100mg/kg+ 1.26% 900-1099mg/kg 0.85% 2000mg/kg

IG 9 9

3.12.IG IG 21.6% IG

2 2 2

IG 6.28% 22 2

IG 2.57%2 2 2

1.4%IG 1.46% 2

2IG 0.53% 2

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-6-

2 2 14IG

IG IG 91.1% 22 2

IG 24.8% 22

IG 12.1%2 2 2

IG 6.5% 22 2

IG 2.6% 22 2 15

3.13.1 14,156 43.5%

8,060 43.3% 6,096 43.8%

168,465 3,187

758 17

3.14.696 2.1% 386 2.1% 310 2.2%

419 1.3%18

214 51.1% 199 47.5% 19

3.15.1,706 5.2% 1,075 5.8%

631 4.5% 10

20

4.

1

http://www.jichi.ac.jp/dph/inprogress/kawasaki/

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-7-

5.

1971.1975; 22 6 : 306-312.

1975; 5 12 : 22-29.1976; 34 2 : 275-283.

-1979; 20 7 : 755-757.

1981;22 1 : 53-58.

-1983; 24 1 : 53-58.

1985; 26 9 : 1049-1053.

1986; 37-51.1987; 28 9 : 1059-1066.

1988; 18-31.1990; 31 5 : 569-576.1992; 33 3 : 309-316.1994; 35 1 : 61-73.1996; 37 4 : 363-383.

1998; 61 3 : 406-420.2000; 63 1 : 121-132.2002; 65 2 : 332-342.

2002.2004; 67 2 : 313-323.2006; 69 2 : 281-292.

1989 20042007; 111 6 : 740-745.

2008; 71 2 : 349-360.20

2010; 73 1 : 143-156.21

2012; 75 3 : 507-523.22

2014; 77 2 : 271-290.23

2016; 79 2 : 273-292.24

2018; 81 2 : 271-274.Kawasaki T, Kosaki F, Okawa S, Shigematsu I, Yanagawa H. A new infantile acute febrilemucocutaneous lymph node syndrome MLNS prevailing in Japan. Pediatrics 1974; 54: 271-276.Yanagawa H, Kawasaki T, Shigematsu I. Nationwide survey on Kawasaki disease in Japan. Pediatrics1987; 80: 58-62.Yanagawa H, Nakamura Y, Yashiro M, Fujita Y, Nagai M, Kawasaki T, Aso S, Imada Y, ShigematsuI. A nationwide survey of Kawasaki disease in 1985-1986 in Japan. J Infect Dis 1988; 158 6 :1296-1301.Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Epidemiologic pictures of Kawasakidisease in Japan: From the nationwide survey in 1991 and 1992. Pediatrics 1995; 95 4 : 475-479.

Page 9: 1* B)¼ - Jichi · 2019-09-25 · 1* c+¬ &É ± Û+« Ë%Ê'2'¼ Ô#. B $ ( b 1 Z K S>&2018 º10 v9 ¥ +« ±18-070 >' 2.0[ ¨ 2.1. H* X í*/ H"á b º N&ã 4# d24 G b ² \1* [ Ì

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Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Results of 12 nationwideepidemiological incidence surveys of Kawasaki disease in Japan. Arch Pediatr Adolesc Med1995; 149: 779-783.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Koyanagi H, Kawasaki T. Update of theepidemiology of Kawasaki disease in Japan, From the results of 1993-94 nationwide survey. JEpidemiol 1996; 6 3 : 148-157.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Tanihara S, Oki I, Zhang T. Results of thenationwide epidemiologic survey of Kawasaki disease in 1995 and 1996 in Japan. Pediatrics 1998;102 6 : e65.Yanagawa H, Nakamura Y, Yashiro M, Oki I, Hirata S, Zhang T, Kawasaki T. Incidence survey ofKawasaki disease in 1997 and 1998 in Japan. Pediatrics 2001; 107 3 : e33.Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Epidemiologic Featuresof Kawasaki Disease in Japan:Results from Nationwide Survey in 2005-2006. J Epidemiol2008; 18(4): 167-172.Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Monthly observation of thenumbers of patients and incidence rates of Kawasaki disease in Japan: results from nationwidesurveys. J Epidemiol 2008; 18(6): 273-279.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Chihara I, Aoyama Y, Kotani K, Yanagawa H.Epidemiologic features of Kawasaki disease in Japan: Results of the 2007-2008 nationwide survey.J Epidemiol 2010; 20(4): 302-307.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Tsuboi S, Aoyama Y, Kotani K, Tsogzolbaatar EO,Yanagawa H. Epidemiologic features of Kawasaki disease in Japan: Results of the 2009-2010nationwide survey. J Epidemiol 2012; 22(2): 216-221.Makino N, Nakamura Y, Yashiro M, Ae R, Tsuboi S, Aoyama Y, Kojo K, Uehara R, Kotani K,Yanagawa H: Descriptive epidemiology of Kawasaki disease in Japan, 2011-2012: from the results ofthe 22nd nationwide survey. J Epidemiol 2015; 25 3 :239-245.Makino N, Nakamura Y, Yashiro Mayum, Sano T, Ae R, Kosami K, Kojo T, Aoyama Y, Kotani,K, Yanagawa H. Epidemiological observation of Kawasaki disease in Japan,2013-2014. PediatricsInternational 2018; 60:581-587.Makino N, Nakamura Y, Yashiro M, Kosami K, Matsubara Y, Ae R, Aoyama Y, Yanagawa H.Nationwide epidemiologic survey of Kawasaki disease in Japan,2015–2016. Pediatrics International2019; 61:397-403.

34 37-41 Journal of Epidemiology http://www.jstage.jst.go.jp/article/jea/35 36 Pediatrics http://www.pediatrics.org/cgi/content/

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196.1176.8

359.1

78.0

215.8

175.4194.7

157.9

402.6

313.4

88.1

67.3

2018

19821986

1979

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NTT

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JA

JCHO

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14

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18

JCHO

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24

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25

26

27

JCHO

28

JCHO

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29

30

31

32

33

34

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37

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39

40

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