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329-0498 3311-1
0285-44-61920285-44-7217
2019 9
-1-
25
1970 2 1 24 1-43
2017 2018 2 25
IG IGIG IG
25 1
1.
25 100100 2017 1 1 2018 12 31 2
241,816
http://www.kawasaki-disease.net/kawasakidata/
2018 10 918-070
2.
2.1.24 2018 12 31
395,238 228,107 167,131 2017 20182017 15,164 8,635 6,529 2018 17,364 9,964 7,400
0-4 10 2017 313.6 348.9 276.5 2018 359.1 402.6313.4 2018 2015 330.2
2.2.
2015 9-10 20151 2016 6-710-11 2016 1
2.3.25 3,785
2,424 2,276 126131 151
-2-
2017 422.2 388.9 385.72018 495.7 436.0 434.62017 134.9 166.7 187 2018 158.1 202.4
252.2 2017 2018
2.4.25,661 78.9% 565 1.7% 6,289
19.3%
2.5.1,604 4.9% 1,042 5.6% 562 4.0%
11 0.03% 117 0.36%1,248 3.84% 2 0.01% 0 0% 283 0.87%
2,901 8.9% 1,850 9.9% 1,051 7.5%35 0.11% 309 0.95%
2,120 6.52% 6 0.02% 4 0.01% 503 1.55%
845 2.6% 548 2.9% 297 2.1%36 0.11% 206 0.63% 488
1.50% 6 0.02% 1 0.003% 164 0.50%
2.6.IG 30,784 94.6% IG 6,06119.7% IG 4,076 13.2%
IG 30,042 97.7% IG 11900-2099mg/kg 29,443 95.7% 900-1099mg/kg
754 2.45% 1 30,141 98.0% 2 5961.94% IG 5 10,710 34.8%
2.7.1 14,156 43.5%
8,465 3,187 758
2.8.696 2.1% 386 2.1% 310 2.2%
419 1.3%
214 51.1% 199 47.5%
3.
3.1.1,816 12 1,804
1,357 75.2Excel 139
27
-3-
1,357 924 68.165.2 95.5
3.2.1
24 2018 12 31 395,238228,107 167,131 2017 2018 2017
15,164 8,635 6,529 2018 17,364 9,964 7,400
2 2,8741 1,900
944956
20-4 10 2017 313.6 348.9 276.5 2018 359.1 402.6
313.4 2018 2015 330.2
2018 / 1.35 1.28
1 1979 1982 1986 31995 2010 12,000
1986 3 2012 1979 12 2013 15,000 1982 2
2016 2017 2018
2 2018 359.1402.6 313.4
3.3.3
2015 9-102015 1 2016 6-7
10-11 2016 12015 2016 1
2013 2018 2 94
3.4.25 2017 2018 2 25
4 71% 109-11 2017 472.2 2018 502.2
24 9-11 24 255
-4-
3.5.0-4 10 3 25
3,7852,424 2,276 126
131 1512017 422.2 388.9 385.7
2018 495.7 436.0 434.62017 134.9 166.7 187 2018 158.1 202.4
252.22017 2018
6 2015 20182018
3.6.25,661 78.9% 565 1.7% 6,289
19.3% 4 4 4,45970.9% 3 23.4% 2 5.1 %
5A 5 2002 2
17 5 65 B 4
3.7.1,478 4.5% 868 4.7% 610 4.4%
1
3.8.2017 2018 6 3 3 6 9
2 1 31 6
3.9.1 1
31,604 4.9% 1,042 5.6% 562 4.0%
11 0.03% 117 0.36%1,248 3.84% 2 0.01% 0 0% 283 0.87%
22,901 8.9% 1,850 9.9% 1,051 7.5%
35 0.11% 309 0.95%2,120 6.52% 6 0.02% 4 0.01% 503 1.55%
2845 2.6% 548 2.9% 297 2.1%
36 0.11% 206 0.63% 488 1.50%6 0.02% 1 0.003% 164 0.50%
-5-
2
3.52.6
27
U 715 1997-1998 20.1%
8
3.10.4 8,192 25.2% 20,679 63.6% 4
2 2 2 67.8% 42 60.3%
IG 5 10,710 34.8% 2 22 75.4% 5 2 67.4%
2 IG 8
3.11.IG 30,784 94.6% 17,608 94.7% 13,17694.6% 9 IG 6,061 19.7%
10IG 4,076 13.2%
3,463 13.8% 6712.7% 546 10.4%
699 17.1%3,447 84.6% 1
1011
IG 30,042 97.7%12 IG 1 1900-2099mg/kg
29,443 95.7% 900-1099mg/kg 754 2.45% 130,141 98.0% 2 596 1.94% 13 IG 1
1900-2099mg/kg 97.1%2100mg/kg+ 1.26% 900-1099mg/kg 0.85% 2000mg/kg
IG 9 9
3.12.IG IG 21.6% IG
2 2 2
IG 6.28% 22 2
IG 2.57%2 2 2
1.4%IG 1.46% 2
2IG 0.53% 2
-6-
2 2 14IG
IG IG 91.1% 22 2
IG 24.8% 22
IG 12.1%2 2 2
IG 6.5% 22 2
IG 2.6% 22 2 15
3.13.1 14,156 43.5%
8,060 43.3% 6,096 43.8%
168,465 3,187
758 17
3.14.696 2.1% 386 2.1% 310 2.2%
419 1.3%18
214 51.1% 199 47.5% 19
3.15.1,706 5.2% 1,075 5.8%
631 4.5% 10
20
4.
1
http://www.jichi.ac.jp/dph/inprogress/kawasaki/
-7-
5.
1971.1975; 22 6 : 306-312.
1975; 5 12 : 22-29.1976; 34 2 : 275-283.
-1979; 20 7 : 755-757.
1981;22 1 : 53-58.
-1983; 24 1 : 53-58.
1985; 26 9 : 1049-1053.
1986; 37-51.1987; 28 9 : 1059-1066.
1988; 18-31.1990; 31 5 : 569-576.1992; 33 3 : 309-316.1994; 35 1 : 61-73.1996; 37 4 : 363-383.
1998; 61 3 : 406-420.2000; 63 1 : 121-132.2002; 65 2 : 332-342.
2002.2004; 67 2 : 313-323.2006; 69 2 : 281-292.
1989 20042007; 111 6 : 740-745.
2008; 71 2 : 349-360.20
2010; 73 1 : 143-156.21
2012; 75 3 : 507-523.22
2014; 77 2 : 271-290.23
2016; 79 2 : 273-292.24
2018; 81 2 : 271-274.Kawasaki T, Kosaki F, Okawa S, Shigematsu I, Yanagawa H. A new infantile acute febrilemucocutaneous lymph node syndrome MLNS prevailing in Japan. Pediatrics 1974; 54: 271-276.Yanagawa H, Kawasaki T, Shigematsu I. Nationwide survey on Kawasaki disease in Japan. Pediatrics1987; 80: 58-62.Yanagawa H, Nakamura Y, Yashiro M, Fujita Y, Nagai M, Kawasaki T, Aso S, Imada Y, ShigematsuI. A nationwide survey of Kawasaki disease in 1985-1986 in Japan. J Infect Dis 1988; 158 6 :1296-1301.Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Epidemiologic pictures of Kawasakidisease in Japan: From the nationwide survey in 1991 and 1992. Pediatrics 1995; 95 4 : 475-479.
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Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Results of 12 nationwideepidemiological incidence surveys of Kawasaki disease in Japan. Arch Pediatr Adolesc Med1995; 149: 779-783.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Koyanagi H, Kawasaki T. Update of theepidemiology of Kawasaki disease in Japan, From the results of 1993-94 nationwide survey. JEpidemiol 1996; 6 3 : 148-157.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Tanihara S, Oki I, Zhang T. Results of thenationwide epidemiologic survey of Kawasaki disease in 1995 and 1996 in Japan. Pediatrics 1998;102 6 : e65.Yanagawa H, Nakamura Y, Yashiro M, Oki I, Hirata S, Zhang T, Kawasaki T. Incidence survey ofKawasaki disease in 1997 and 1998 in Japan. Pediatrics 2001; 107 3 : e33.Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Epidemiologic Featuresof Kawasaki Disease in Japan:Results from Nationwide Survey in 2005-2006. J Epidemiol2008; 18(4): 167-172.Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Monthly observation of thenumbers of patients and incidence rates of Kawasaki disease in Japan: results from nationwidesurveys. J Epidemiol 2008; 18(6): 273-279.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Chihara I, Aoyama Y, Kotani K, Yanagawa H.Epidemiologic features of Kawasaki disease in Japan: Results of the 2007-2008 nationwide survey.J Epidemiol 2010; 20(4): 302-307.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Tsuboi S, Aoyama Y, Kotani K, Tsogzolbaatar EO,Yanagawa H. Epidemiologic features of Kawasaki disease in Japan: Results of the 2009-2010nationwide survey. J Epidemiol 2012; 22(2): 216-221.Makino N, Nakamura Y, Yashiro M, Ae R, Tsuboi S, Aoyama Y, Kojo K, Uehara R, Kotani K,Yanagawa H: Descriptive epidemiology of Kawasaki disease in Japan, 2011-2012: from the results ofthe 22nd nationwide survey. J Epidemiol 2015; 25 3 :239-245.Makino N, Nakamura Y, Yashiro Mayum, Sano T, Ae R, Kosami K, Kojo T, Aoyama Y, Kotani,K, Yanagawa H. Epidemiological observation of Kawasaki disease in Japan,2013-2014. PediatricsInternational 2018; 60:581-587.Makino N, Nakamura Y, Yashiro M, Kosami K, Matsubara Y, Ae R, Aoyama Y, Yanagawa H.Nationwide epidemiologic survey of Kawasaki disease in Japan,2015–2016. Pediatrics International2019; 61:397-403.
34 37-41 Journal of Epidemiology http://www.jstage.jst.go.jp/article/jea/35 36 Pediatrics http://www.pediatrics.org/cgi/content/
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196.1176.8
359.1
78.0
215.8
175.4194.7
157.9
402.6
313.4
88.1
67.3
2018
19821986
1979
-22-
-23-
-24-
-25-
-26-
NTT
JAJAJAJAJAJCHO
KKR
-27-
JA
JCHO
10
11
JCHO
TMG
12
13
NTTJR
-28-
14
AOI
15
JA
16
JCHO
17
JCHO
-29-
18
JCHO
19
20
21
JA
22
JAJA
23
AOI
JCHO
-30-
24
JCHO
25
26
27
JCHO
28
JCHO
-31-
29
30
31
32
33
34
JR
35
JCHO
36
37
38
-32-
39
40
41
42
-
43
44
45
46
47
-33-