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A XXV-a Conferinta Nationala SRIE
PROGRAM
14 nov. 2017 Curs preconferinta Epilepsia prin cazuri
clinice (Preconference course Epilepsy hands on)
Tutori:
Iuliu Bacos
Diana Barca
Niculina Butoianu
Laura Craciun
Dana Craiu
Catrinel Iliescu
Cristina Motoescu
Cristina Pomeran
Irina Popa
Carmen Sandu
Mihaela Vintan
Walter van Emde Boas
Descrierea cursului:
Acest curs este dedicat tinerilor neurologi si neurologi pediatri pentru a invata sa investigheze si sa trateze epilepsia
din cazurile clinice reale. Partea a doua este potrivita si pentru pediatri si medicii de familie. Concluziile cazurilor au
la baza date din literatura care sustin afirmatiile facute in rezolvarea cazurilor.
Cazuri/situatii/scenarii practice – vor fi oferite sub forma de discutii interactive de catre speakeri – cursantii vor
raspunde. Audienta va fi impartita pe grupe de 5-6 cursanti care vor discuta cazurile. Fiecare grupa va prezenta propria
opinie (5 min) la sfarsit cazul va fi discutat de tutori.
Premii:
Cele mai bune raspunsuri vor fi punctate.
Echipa cu cele mai bune raspunsuri va castiga taxa de participare pentru Cursul Est-European de
Epileptologie din Ukraina.
Lucru pe echipe – caz clinic (10 grupe x 5 + tutore care ii indruma) – formulare concluzii
(working groups of 5 persons and one tutor)
PROGRAM CURS:
08.00 – 08.45 – Inregistrare participanti (registration)
08.45 – 09.00 – Deschiderea cursului si prezentarea participantilor si a modalitatii de lucru (Course
opening and participants presentation; working modality explanations) – Dana Craiu, Iuliu Bacos, Diana
Barca, Catrinel Iliescu, Mihaela Vintan
09.00 – 11.00 – EEG – stim cum sa folosim? (EEG – do we know how to use it?)
Moderatori: Oana Tarta-Arsene, Cristina Pomeran
09.00 – 09.40 – Oana Tarta Arsene – Artefacte EEG (EEG Artifacts)
09.40 – 10.20 – Irina Popa, Mihai Malaia, Ioana Mindruta – Testarea pacientior in criza epileptica
10.20 – 11.00 - Cristina Pomeran: Rolul EEG in practica clinica la copil
(The role of EEG in clinical practice in children)
11.00 – 11.30 – Pauza cafea (Coffee break)
11.30 – 13.00 – Dificultati de diagnostic in practica clinica (Diagnosis difficulties in clinical practice)
Moderatori: Iuliu Bacos, Laura Popescu
11.15 – 11.40 – Cristina Pomeran: Rolul EEG in diagnostic – caz clinic
(Role of EEG for diagnosis – clinical case)
11.40 – 12.05 – Laura Popescu: Situatii clinice in practica zilnica. Tu ce ai face?
(Clinical situations scenarios in daily practice. What would you do?)
12.05 – 12.30 – Mihaela Vintan: Cum gandim un caz de epilepsie asociat cu tulburari de miscare?
(How do we think of a case of epilepsy associated with movement disorders?)
12.30 – 13.00 – Iuliu Bacos: Epilepsie focala, deficienta motorie pentru diagnostic etiologic
(Focal epilepsy and motor deficit - etiological diagnosis)
13.00 – 14.00 – Masa de pranz (Lunch)
14.00 – 15.40 – Discutii interactive de cazuri si situatii clinice
(Interactive discussions of clinical scenarios and cases)
Audienta se imbogateste cu medici de familie si se discuta cateva idei pe baza de cazuri clinice
(The audience adds to family doctors and discuss some ideas based on clinical cases)
Moderatori: Dana Craiu, Adrian Toma
14.00 – 14.15 – Catrinel Iliescu – Proiectul ESBACE
14.15 – 14.45 – Adrian Toma – Convulsiile la nou nascut dupa externarea din maternitate. La ce se
poate astepta medicul de familie?
(Seizures in neonates beyond the neonatal ward. What can the GP encounter?)
14.45 – 15.15 – Dana Craiu: Fenomene paroxistice la copil – discutii interactive pe baza cazurilor
clinice
(Paroxystic events in children - interactive discussions based on clinical cases)
15.15 – 15.45 – Laura Craciun: Epilepsia in practica clinica la adult
(Epilepsy in clinical practice in adults)
15.45 – 16.15 – Pauza cafea (Coffe-Break)
16.15 – 18.40 – Discutii interactive de cazuri si situatii clinice
(Interactive discussions of clinical scenarios and cases)
Moderatori: Mihaela Vintan, Catrinel Iliescu
16.15 – 16.35 – Carmen Sandu: Tratam sau nu tratam?
(Should we treat or not?)
16.35 – 16.55 – Madalina Leanca: Ce tratament aleg?
(What treatment should I choose?)
16.55 – 17.15 – Niculina Butoianu: Convulsiile febrile: cum investigam?
(Febrile seizures – how to investigate?)
17.15 – 17.35 – Diana Barca: Convulsiile febrile – cand trimitem si cand nu trimitem la neurologul
pediatru?
(Febrile seizures – when to send to pediatric neurologist and when not?)
17.35 – 17.55 – Catrinel Iliescu: Cum urmarim un pacient cu epilepsie?
(How to follow a patient with epilepsy?)
17.55 – 18.40 – Walter van Emde Boas. Video-EEG – discutii interactive de cazuri.
(Video-EEG – interactive case discussions).
Discutii si inchiderea cursului (Discussions and closure)
15 nov. 2017. Conferinta – ZIUA 1
(Conference – Day 1)
08.30 – 09.00 Cuvant de bun venit; Deschidere; Istoria SRIE
(Wellcome; opening; SRIE history)
Dana Craiu, Radu Rogozea, Voica Foisoreanu, Ileana Benga
09.00 – 11.00 Ce este nou in epileptologie: definitii si clasificare, tratament
(What is new in Epilepsy: deffinitions and classification)
Chairs: Ioana Mindruta, Dragoslav Sokic
09.00 – 09.45 Walter van Emde Boas: Ce e nou in clasificarea si terminologia in epilepsiei? Ce termeni nu
mai folosim si de ce? Cum se schimba clasificarea epilepsiilor ?
(What is new in definition and classification of epilepsy? Which terms should we not use and why?
How is classification of seizures and syndromes change?)
09.45 – 10.15 Dragoslav Sokic: Cum se schimba definitia si clasificarea statusului epileptic?
(How is changing the definition and classification of status epilepticus?)
10.10 – 10.35 Ioana Mindruta: Conectivitatea functionala – cunostinte despre retelele epileptogenice.
(Functional connectivity - gaining insight in the epileptogenic networks)
10.35 – 11.00 Carmen Burloiu: Tratamentul cu Everolimus ca indicatie pentru epilepsie – care sunt
dovezile?
(Everolimus for epilepsy treatment – what is the evidence?)
11.00 – 11.30 Pauza cafea
11.30 – 13.00. Cum investigam? (How to investigate?)
Chairs: Voica Foisoreanu, Oreste Straciuc
11.30 – 11.50 Diana Barca: Cum investigam epilepsia din bolile metabolice?
(How to investigate metabolic disorders?)
11.50 – 12.20 Eugen Tarta-Arsene: Imagistica structurala cerebrala in epilepsie.
(Immaging structural causes of epilepsy)
12.20 – 12.40 Florin Preoteasa, Eugen Tarta-Arsene, Oana Tarta-Arsene: Evaluarea imagistica prin IRM
functional in epilepsie.
(Functional MRI in epilepsy)
12.40 - 13.00 Oreste Straciuc: FDG PET-CT in epilepsie – perspectiva radiologului.
(FDG-PET-CT in epilepsy – radiologist perspective)
13.00 – 14.00: Masa de pranz (Lunch)
14.00 – 16.00. Investigarea genetica in epilepsie – where are we?
(Genetic investigations in epilepsy – where are we?)
Chairs: Dorota Hoffman-Zacharska, Magdalena Budisteanu
14.00 – 14:30 Dorota Hoffman-Zacharska (Department of Medical genetics; Institut of Mother and
Child, Warsaw Poland): Panelurile NGS – noua metoda pentru diagnosticul Encefalopatiilor epileptic cu
debut precoce; noi posibilitati si problem
(NGS panels - new way of Early Infantile Epileptic Encephalopthies diagnostic; new possibilities
and problems).
14.30 – 14.50 Magdalena Budisteanu, Diana Barca, Catrinel Iliescu, Sorina Mihaela Papuc, Andreea
Tutulan-Cunita, Aurora Arghir, Dana Craiu: Epilepsia la copiii cu sindrom Angelman. Experienta Clinicii
de Neurologie Pediatrica a Spitalului Clinic de Psihiatrie Prof. Dr. Al. Obregia.
(Epilepsy in Angelman Syndrome. Single center experience – Pediatric Neurology Clinic, Alexandru
Obregia Hospital)
14.50 – 15.10 Sorina Mihaela Papuc, Katharina Steindl, Pascal Joset, Lucia Abela, Beatrice Oneda, Luke
Simmons, Déborah Mathis, Bernhard Schmitt, Gabriele Wohlrab, Lisa Crowther, Markus Zweier, Laura
Gogoll, Michael Papik, Barbara Plecko, Anita Rauch. Investigația genomică în encefalopatiile epileptice.
(Genomic investigation in epileptic encephalopathies)
15.10 – 15.30 Mona Gandea, Marga Buzatu (Hopital Universiatiare Clinique Chraleroi, Belgium).
Encefalopatia cu epilepsie STXBP1 – importanta diagnosticului genetic in cazurile severe de epilepsie
(STXBP1 Encepahlopathy with epilepsy- importance of genetic diagnostic in severe cases of
epilepsy)
15.30 -15.50 Dana Craiu. Rolul investigarii genetice in tratamentul de precizie al epilepsiei.
(The role of genetic investigation in precision treatment of epilepsy)
15.50 – 16.05 Radu Ursu, Viorica Radoi. Testarea genetica in epilepsie. Ce ar trebui sa facem?
(Genetic testing in epilepsies. What should we be doing?)
16.05 – 16.30: Pauza de cafea
(Coffee break)
16.30 – 18.00: Noutati in electrofiziologie in epilepsie
(New research in neurophysiology in epilepsy)
Chairs: Anna Kelemen, Tudor Lupescu
16.30 – 17.00 Sandor Beniczky: Source imaging electromagnetic in epilepsie
(Electromagnetic source imaging in clinical practice).
17.00 – 17.20 Anna Kelemen: Valoarea analizei de somn in epilepsie
(The value of sleep analysis in epilepsy).
17.20 – 17.40 Tudor Lupescu, Ana Maria Cobzaru, Ionela Codiță, Ioana Mînduță, Mihai Moldovan Izabela
Popa: Modificări ale excitabilității axonului motor în cursul terapiei antiepileptice cu blocante ale canalelor
de sodiu voltaj-dependente
(Changes of motor neuron excitability during antiepileptic treatment with voltage dependant
sodium blockers).
17.40 – 18.00 Bogdan Amuzescu, George Cocină, Ştefan Florică, Vasile Cîrlig, Alice Dascălu:
Proiectarea, construcţia şi testarea unui sistem EEG cu 8 canale pentru înregistrări de suprafaţă la animale
mici (Designing, building and testing a 8 channels surface EEG system for small laboratory animals
recordings)
18.00 – 19.00 – Adunarea generala a membrilor SRIE
(SRIE General Assembley)
16 nov. 2017. Conferinta – ZIUA 2
(Conference – Day 2) 09.00 – 11.00 Ce este nou in diagnosticul si tratamentul epilepsiei?
(What is new in diagnostic methods and therapy in epilepsy?)
Chairs: Aleksandar Ristic, Adriana Dulamea
09.00 – 09.30 Adriana O Dulamea, E Solomon, C Vilciu, C Banica, Ana Campeanu – Epilepsia asociata
patologiei neurologice cu mecanism autoimun
(Epilepsy in neurological diseases with autoimmune mechanism)
09.30 – 10.00 Dana Craiu – Canabisul medicinal – care sunt dovezile?
(Medicinal Canabis – what are the proofs?)
10.00 – 10.30 Oana Tarta-Arsene, Cristina Motoescu, Catrinel Iliescu, Nina Butoianu, Alice Dica, Dana
Craiu, Ioana Mindruta, Sergiu Stoica (Bucuresti): Aspecte practice ale epilepsiilor asociate displaziilor
corticale la copil
(Practical aspects of the pilepsies associated to cortical dysplasias in children)
10.30 – 11.00 Stefano Francione – Termocoagularea cu radiofrecventa la finalul investigarii SEEG –
tratament si instrument diagnostic suplimentar
(Radiofrequency thermocoagulation at the end of SEEG exploration – treatment and a
supplementary diagnostic tool)
11.00 – 11.30 Pauza cafea
(Coffee break)
11.30 – 13.30. Femeia cu epilepsie
(The woman with epilepsy)
Chairs: Cristina Panea, Dana Ruxandra Chirileanu
11.30 – 12.00 Dana Ruxandra Chirileanu (Timisoara): Valproatul de sodiu in tratamentul femeii cu
epilepsie – ce este nou?
(Valproate in the treatment of women with epilepsy – what is it new?)
12.00 – 12.30 Cristina Panea (Bucuresti): Cum investigam femeia cu epilepsie inainte si in timpul sarcinii?
(How to investigate the woman with epilepsy before and during pregnancy?)
12.30 – 13.00 Alina Blesneag (Cluj-Napoca): Noile MAE in tratamentul femeii cu epilepsie – date recente
din registrele de sarcina
(New Antiepileptic drugs for treatment of women with epilepsy: new data from pregnancy registries)
13.00-13.30 Radu Vladareanu – Nasterea la femeia cu epilepsie
(Birth in women with epilepsy)
13.30 – 14.30 Masa de pranz
(Lunch)
14.30 – 16.00. Sindromul Dravet – din nou in lumina reflectoarelor
(Dravet syndrome – again in the spotlight)
Chairs: Dana Craiu, Mihaela Vintan
14.30 – 14.50 Mihaela Vintan (Cluj Napoca): Aspecte clinice in sindromul Dravet
(Clinical aspects in Dravet Syndrome)
14.50 – 15.10 Cristina Anghelescu: Genetica sindromului Dravet
(Genetics of Dravet Syndrome)
15.10 – 15.30 Dana Craiu: Tratamentul statusului epileptic in sindromul Dravet
(Treatment in status epilepticus in Dravet syndrome)
15.30 – 16.00 LANSARE DE CARTE – “Primele 20 de intrebari despre SINDROMUL DRAVET”
(The first 20 questions about Dravet Syndrome)– Autori Charlotte Dravet, Stephane Auvin, Domenica
Battaglia, Ana Isabel Dias, Marina Nikanorova, Rocio Sanchez-Carpintero, Katalin Sterbova (Scrisa
cu sprijinul BIOCODEX), Editata John Libbey Eurotext. (cartea este destinata medicilor in sprijinul
pacientilor cu boala Dravet si este tardusa in limba Romana)
16.00 – 16.30 Pauza de cafea
(Coffee break)
16.30 – 18.10: Epilepsie pediatrica si noutati in epileptologie
(Pediatric epilepsy and new data in epilepsy)
Chairs: Alexandru Vlad Ciurea, Kees Braun
16.30 – 16.50 A V Ciurea, Ionut Luca-Husti, Aurel Mohan, Andrei Marinescu, Razvan Onciul. Crizele
de epilepsie la copil. Elemente de debut in chistele arahnoidiene intracraniene. Experinta pe 417 cazuri
(Seizures in childhood. Onset signs in intracranian arachnoid cysts.417 cases experience)
16.50 - 17.10 Aleksandar Ristic – Noutati in neuroimagistica – postprocesarea (Recent advances in
neuroimaging with emphasis on postprocessing)
17.10 – 17.40 Kees Braun (Utrecht, Olanda): Chirurgia epilepsiei la copil: indicatii si prognostic
(Pediatric epilepsy surgery: indications and outcome)
17.40 – 18.10 Petia Dimova (Sofia, Bulgaria). Epilepsia in encefalitele autoimune
(Epilepsy in autoimmune encephalitis).
17 Nov. 2017. Course: Investigating resistant epilepsy
08.0 – 08.30: Registration & opening remarks
Chairs: Philippe Kahane & Dana Craiu
08.30 – 09.00 Kees Braun: Structural imaging in presurgical evaluation
09:00 – 09.30 Dragoslav Sokic - Presurgical evaluation in HS
09.30- 10.00 Aleksandar Ristic: Presurgical evaluation in FCD
10.00 -10.30 Petia Dimova: Surgical treatment in genetic epilepsies
10.30 – 11.00: Coffee break
Chairs: Philippe Kahane & Ioana Mindruta 11.00 – 11.30 Lorella Minotti - Epilepsy surgery in orbitofrontal cortex
11.30 - 12.00 Philippe Kahane - Epilepsy surgery in insular cortex
12.00 - 12.30 Stefano Francione: Epilepsy surgery in posterior cortex
12.30 – 13.00 Carmen Barba: Surgery for epileptic encephalopathies: who is the best candidate
13.00 - 14.00 Lunch
17-18 Noiembrie 2017: U-Task Meeting
Avem marele privilegiu ca in anul acesta sa gazduim in Bucuresti intalnirea Grupului de lucru de chirurgie
a epilepsiei. Acest grup da prilejul discutiei cazurilor reale de epilepsie rezistenta la tratament care ar
putea avea solutie chirurgicala. Sunt discutate si rezultate ale interventiilor chirurgicale pentru epilepsie
pentru un bun feed-back.
Gazda romana este Dr Ioana Mindruta, coordonatoarea Programului National de tratament al Epilepsiilor
Rezistente in Romania.
Este un prilej in care tinerii epileptologi se pot intalni cu epileptologi experimentati carora pot sa le puna
intrebari, de la care pot invata si pot sa discute informal problem de care se lovest in fiecare zi in practica
clinica.
Se discuta probleme de rutina dar si tehnici si interventii de varf.
Un regal in chirurgia epilepsiei!
Expertii pe care ii puteti intalni sunt: Alexis Arzimanoglou, Lorella Minotti, Philippe Kahane, Stefano
Francione, Kees Braun, Floor Jansen, Petia Dimova, Carmen Barba, etc
Programul U-Task se intinde pe doua jumatati de zi, cate 4 ore in fiecare zi:
17 Noiembrie : 14.00 – 18.30
13.00 – 14.00 – Lunch
14.00 – 16.00 – prezentari de cazuri ale participantilor
16.00 – 16.30 – Coffee break
16.30 – 18.30 – prezentari de cazuri ale participantilor
18. Noiembrie: 09.00 – 13.00
09.00 – 11.00 – prezentari de cazuri ale participantilor
11.00 – 11.30 – Coffee break
11.30 – 13.30 – prezentari de cazuri ale participantilor
13.30 – 14.30 – Lunch
18 Noiembrie 2017:
Aspecte sociale in epilepsie - intalnire SRIE – Asociatia
Dravet (14.00 – 17.00)
Aceasta parte din conferinta vizeaza discutarea unor aspecte practice de tratament si ingrijire in sindromul
Dravet cu medicii neurologi pediatri si pediatri, avand invitati membrii asociatiei Dravet.
14.00 – 14.30 Ileana Mardare: Accesul pacientilor la medicamente in Romania: misiune imposibila? (Access
of patients to AEDs in Romania: mission impossible?)
14.30 – 15.00 Dana Craiu: Tratamentul in statusul epileptic in sindromul Dravet
(Treatment in SE in Dravet)
15.00 – 15.30 Carmen Sandu: Rolul Canabidiol in tratamentul Sindromului Dravet si al epilepsiilor
rezistente (The role of Cannabidiol (CBD) in epilepsy treatment in Dravet syndrome and resistant
epilepsies)
15.30 -16.00 Cristina Anghelescu. Template al protocolului de urgenta la copilul cu sindrom Dravet
(Emergency protocol template in Dravet Syndrome)
16.00 – 16.30 Dana Craiu: Vaccinarea la copiii cu syndrome Dravet – discutarea protocolului propus pentru
vaccinare (Vaccination in Dravet patients – discussions on the proposed vaccination protocole)
16.30 – 17.00 Ce publicatii sunt disponibile in Romania pentru Syndromul Dravet? (what publications are
available in Romanian language for Dravet Syndrome)
- “Primele 20 de intrebari despre SINDROMUL DRAVET” (The first 20 questions about Dravet
Syndrome)– Autori Charlotte Dravet, Stephane Auvin, Domenica Battaglia, Ana Isabel Dias, Marina
Nikanorova, Rocio Sanchez-Carpintero, Katalin Sterbova (Scrisa cu sprijinul BIOCODEX), Editata John
Libbey Eurotext. (cartea este destinata medicilor in sprijinul pacientilor cu boala Dravet si este tardusa in
limba Romana)
- Cartea despre Supereroi