Arrhythmogenic right ventricular dysplasia in emergency department A 43-year-old man presented to the emergency department with haemodynamically compromised ventricular tachycardia neces- sitating electrical cardioversion. Classical ‘‘epsilon waves’’ noted on his initial electrocardiogram prompted an evaluation for arrhythmogenic right ventricular dysplasia. The diagnosis was confirmed with echocardiography and magnetic resonance imaging of the heart. A prompt recognition and management of this condition in the emergency department helped prevent significant mortality that may be associated with arrhythmogenic right ventricular dysplasia. A 43-year-old man was admitted to a regional hospital elsewhere with a history of recurrent palpitations, syncope and ventricular tachycardia (VT). He was started on amiodarone, required cardioversion several times for termination of VT and was finally transferred to our hospital. He presented to the emergency department (ED) with palpitations and hypotension (BP = 80/60 mm Hg). The 12-lead ECG showed wide QRS tachycardia suggesting monomorphic VT (180 bpm) of left bundle-branch block (BBB) morphology with left-axis deviation. The patient was cardioverted immediately with 200 J. The ECG during sinus rhythm showed a discrete wave (epsilon wave) just beyond the QRS complex 1 and inverted T waves in the right precordial leads (fig 1). On the basis of the ECG, a diagnosis of arrhythmogenic right ventricular dysplasia (ARVD) was considered, which was confirmed by echocardiogram and magnetic resonance imaging. He was started on sotalol and subsequently underwent ICD insertion. ARVD is an under-recognised clinical entity characterised by ventricular arrhythmias and a specific ventricular pathology. The ECG is the initial investigation in the diagnostic approach of this disease. A pattern of incomplete or complete right BBB, the epsilon wave and T inversion in precordial leads are typical ECG findings in these patients. Given its uncommon occur- rence and first presentation often being in ED, it is important for ED physicians to be aware of its presentation, classical ECG findings and management. M Rao, 1 P Prashanth, 2 M K Mukhaini 2 1 Department of Emergency Medicine, Royal Hospital, Muscat, Oman; 2 Department of Cardiology, Royal Hospital, Muscat, Oman Correspondence to: Dr M Rao, Department of Emergency Medicine, Royal Hospital, Post Box 1331, Muscat-111, Oman; [email protected] Competing interests: None. Provenance and peer review: Received :50. doi:10.1136/ha.2009.000877 REFERENCE 1. Hurst JW. Naming of the waves in the ECG, with a brief account of their genesis. Circulation 1998;98:1937–42. Figure 1 Electrocardiogram during sinus rhythm showing epsilon waves (arrows) in lead V1. Images in cardiovascular medicine Heart Asia 2009 50 Heart Asia 2009 on September 15, 2020 by guest. Protected by copyright. http://heartasia.bmj.com/ Heart Asia: first published as 10.1136/ha.2009.000877 on 5 July 2010. Downloaded from

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Page 1: Arrhythmogenic right ventricular dysplasia in emergency ... · ARVD is an under-recognised clinical entity characterised by ventricular arrhythmias and a specific ventricular pathology

Arrhythmogenic right ventriculardysplasia in emergency department

A 43-year-old man presented to the emergency department withhaemodynamically compromised ventricular tachycardia neces-sitating electrical cardioversion. Classical ‘‘epsilon waves’’ notedon his initial electrocardiogram prompted an evaluation forarrhythmogenic right ventricular dysplasia. The diagnosis wasconfirmed with echocardiography and magnetic resonanceimaging of the heart. A prompt recognition and managementof this condition in the emergency department helped preventsignificant mortality that may be associated with arrhythmo-genic right ventricular dysplasia.

A 43-year-old man was admitted to a regional hospitalelsewhere with a history of recurrent palpitations, syncope andventricular tachycardia (VT). He was started on amiodarone,required cardioversion several times for termination of VT andwas finally transferred to our hospital. He presented to theemergency department (ED) with palpitations and hypotension(BP = 80/60 mm Hg). The 12-lead ECG showed wide QRStachycardia suggesting monomorphic VT (180 bpm) of leftbundle-branch block (BBB) morphology with left-axis deviation.The patient was cardioverted immediately with 200 J. The ECGduring sinus rhythm showed a discrete wave (epsilon wave) justbeyond the QRS complex1 and inverted T waves in the rightprecordial leads (fig 1).

On the basis of the ECG, a diagnosis of arrhythmogenic rightventricular dysplasia (ARVD) was considered, which was con-firmed by echocardiogram and magnetic resonance imaging. Hewas started on sotalol and subsequently underwent ICD insertion.ARVD is an under-recognised clinical entity characterised byventricular arrhythmias and a specific ventricular pathology.The ECG is the initial investigation in the diagnostic approachof this disease. A pattern of incomplete or complete right BBB,the epsilon wave and T inversion in precordial leads are typicalECG findings in these patients. Given its uncommon occur-rence and first presentation often being in ED, it is importantfor ED physicians to be aware of its presentation, classical ECGfindings and management.

M Rao,1 P Prashanth,2 M K Mukhaini2

1 Department of Emergency Medicine, Royal Hospital, Muscat, Oman; 2 Department ofCardiology, Royal Hospital, Muscat, Oman

Correspondence to: Dr M Rao, Department of Emergency Medicine, Royal Hospital,Post Box 1331, Muscat-111, Oman; [email protected]

Competing interests: None.

Provenance and peer review: Received

:50. doi:10.1136/ha.2009.000877

REFERENCE1. Hurst JW. Naming of the waves in the ECG, with a brief account of their genesis.

Circulation 1998;98:1937–42.

Figure 1 Electrocardiogram during sinus rhythm showing epsilon waves (arrows) in lead V1.

Images in cardiovascular medicine

Heart Asia 200950

Heart Asia 2009