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Malformaiile faringelui
Dan Cristian Gheorghe
Insuficienta velo-palatina
Congenitala Secundara (dobandita)
Tratament: UPPP logopedie
Palatoschizis
Izolat In cadrul unor sindroame congenitale Pierre-Robin
Maladia Crouzon
Tiroida ectopic
Defect de coborre a glandei tiroide n viaa fetal
Incidena: Raport pe sexe: 3-4/1 (femei) 1:4000 1:8000
Localizri
Baza limbii Submandibular Laringian Traheal Mediastinal Esofagian Mediastinal Intracardiac
Clinic
Asimptomatic Senzaie de corp strin Dispnee Disfonie Hemoragii severe(1)
1. Chiu, T. T., et al. (2002). "Massive bleeding from an ectopic lingual thyroid follicular adenoma during pregnancy." Am J Otolaryngol 23(3): 185-188.
Explorri
Dozare hormoni tiroidieni: T3, T4, fraciile libere de T3 i T4, TSH
Ecografia regiunii cervicale Scintigrafia cu Tc-99m CT, RMN (n indicaii chirurgicale) Biopsia aspirativ cu ac fin (+/- ecografie)?
Tratament
Monitorizare pacient asimptomatic Exerez chirurgical:
Hemoragii severe Tulburari de respiraie/deglutiie Malignizare
Evoluie
Risc malignizare crescut (discuii)?(1,2)
1. Cherif, L., et al. (2004). "[Ectopic thyroid: two cases]." Ann Endocrinol (Paris) 65(3): 233-237. 2. Klubo-Gwiezdzinska, J., et al. (2011). "Clinical review: Ectopic cervical thyroid carcinoma--review of the
literature with illustrative case series." J Clin Endocrinol Metab 96(9): 2684-2691.
Chistele latero-cervicale (branhiale)
Pe marginea anterioara a scm
Tratament: chirurgical
Chistul de tract tireoglos
Fistula de tract tireoglos