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Final Diagnosis Intralobar Pulmonary Sequestration

Final Diagnosis Intralobar Pulmonary Sequestration

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Page 1: Final Diagnosis Intralobar Pulmonary Sequestration

Final Diagnosis

Intralobar Pulmonary Sequestration

Page 2: Final Diagnosis Intralobar Pulmonary Sequestration

8/15/2005

Page 3: Final Diagnosis Intralobar Pulmonary Sequestration
Page 4: Final Diagnosis Intralobar Pulmonary Sequestration
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History of recurrent pneumonia

Page 6: Final Diagnosis Intralobar Pulmonary Sequestration

Surgical Report

• Intralobar Pulmonary Sequestration, treated with right lower lobectomy

• Two major arteries from the thoracic aorta• Large vein draining sequestered lobe

Page 7: Final Diagnosis Intralobar Pulmonary Sequestration
Page 8: Final Diagnosis Intralobar Pulmonary Sequestration
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Bronchopulmonary Sequestration

Definition• Non-functioning lung tissue • Separated from normal bronchial tree• Vascularized by a systemic artery

Two Forms• Intralobar (ILS): within the visceral pleura• Extralobar (ELS): separated from the lung by its

own pleura

Page 14: Final Diagnosis Intralobar Pulmonary Sequestration

Intralobar Pulmonary Sequestration (ILS)

Characteristics• More common type• May present at any age• Generally as recurrent infection• No sexual predominance• Almost exclusively affects lower lobe• Arterial supply: descending aorta• Venous drainage: pulmonary veins

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Etiology of Bronchopulmonary

Sequestration

• Accessory bud that forms caudal to lung buds• Traction theory• Postnatal formation

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Pulmonary SequestrationComplications

• Recurrent infection

• Heart failure

• Intralobar malignancy

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Treatment of Pulmonary Sequestration

Symptomatic Disease

• Surgery: lobectomy or segmental resection

• Arterial embolization

Page 18: Final Diagnosis Intralobar Pulmonary Sequestration

Patient Follow-up

• Given granulomas and acid fast bacilli, sputum was sent for culture. Three sputum samples were negative for acid fast bacilli. A ppd was placed and was also negative.

• Patient was treated empirically with IRPE for four months.