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Handout modified from: Quillen DA, Blodi, BA, and Bennett TJ. Clinical Features of Retinal Disease. Quillen DA and Blodi BA, eds. Clinical Retina. Chicago: AMA Press, 2002. Clinical Features of Retinal Disease __________________ David A. Quillen, MD Penn State College of Medicine Barbara A. Blodi, MD University of Wisconsin-Madison

Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

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Page 1: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

Handout modified from:

Quillen DA, Blodi, BA, and Bennett TJ. Clinical Features of Retinal Disease. Quillen DA and Blodi BA,

eds. Clinical Retina. Chicago: AMA Press, 2002.

Clinical Features of

Retinal Disease

__________________

David A. Quillen, MD Penn State College of Medicine

Barbara A. Blodi, MD University of Wisconsin-Madison

Page 2: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 71

T A B L E 1

Clinical Features of Retinal Disease

Bull’s Eye Maculopathy Cherry Red Spot Choroiretinal Folds

Macular Diseases Age-Related Macular Age-Related MacularDegeneration Degeneration

Macular Hole (chronic) Hypotony Maculopathy

Pattern Dystrophy IdiopathicChorioretinal Folds

Posterior Microphthalmos

Retinal Vascular Diseases Central Retinal Artery Occlusion

Hereditary Disorders Stargardt Disease Tay-Sachs Disease

Cone Dystrophy Niemann-Pick Disease

Retinitis Pigmentosa Cherry Red Spot Myoclonus

Fenestrated Sheen Macular Dystrophy

Concentric Annular Macular Dystrophy

Drug Toxicities Chloroquine/ Gentamicin ToxicityHydroxychloroquine

Fomivirsen

Inflammatory Diseases Acute Macular Posterior Scleritis Neuroretinopathy

UAIM

Tumors

Trauma Commotio Retinae

Peripheral Retinal Diseases

Vitreous

Other Papilledema

Optic Disc Drusen

Retrobulbar Tumor

continued

Page 3: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

72 C H A P T E R 3 Clinical Features of Retinal Disease

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Choroidal Cotton Wool Spot Cystoid Macular EdemaNeovascularization

Macular Diseases Age-Related Macular Age-Related MacularDegeneration Degeneration

Myopia Post-Intraocular Surgery CMEAngioid Streaks Epiretinal MembranePattern Dystrophy Vitreoretinal Traction SyndromePolypoidal Choroidal Hypotony Maculopathy

VasculopathyIdiopathic

Retinal Vascular Diseases Diabetic Retinopathy Diabetic RetinopathyHypertensive Retinopathy Branch Retinal Vein OcclusionRetinal Vascular Occlusions Central Retinal Vein OcclusionLeukemic RetinopathyRadiation RetinopathyAnemiaBone Marrow

Transplantation

Hereditary Disorders Best’s Disease Retinitis PigmentosaStargardt Disease X-Linked Juvenile RetinoschisisGyrate AtrophyRetinitis Pigmentosa

Drug Toxicities Interferon Toxicity Latanoprost-related CMENicotinic Acid MaculopathyEpinephrine Reaction

Inflammatory Diseases POHS HIV Retinopathy Birdshot ChorioretinopathyMultifocal Choroiditis CMV Retinopathy Intermediate UveitisSerpiginous Choroiditis Systemic Lupus Idiopathic Vitritis

ErythematosusBehçet’s DiseaseGiant Cell ArteritisPolyarteritis NodosaCat Scratch Disease

Tumors Choroidal Nevus Choroidal MelanomaChoroidal Osteoma

Trauma Choroidal Rupture Purtscher’s RetinopathyBlunt Trauma

Peripheral Retinal Diseases Chronic Retinal Detachment

Vitreous

Other Laser PhotocoagulationOptic Disc Drusen

Page 4: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 73

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Drusen Flecked Retina Foveal Yellow SpotSyndromes

Macular Diseases Age-Related Macular Macular Hole, Stage IDegeneration

Central SerousChorioretinopathy

Choroidal Neovascularization

Cystoid Macular Edema

Pattern Dystrophy

Solar Retinopathy

Age-Related MacularDegeneration (Drusen)

Retinal Vascular Diseases Diabetic Retinopathy

Toxemia of Pregnancy

Branch Retinal Vein Occlusion

Central Retinal Vein Occlusion

Hereditary Disorders North Carolina Stargardt DiseaseMacular Dystrophy

Fundus Albipunctatus

Dominant Drusen Flecked Retina of Kandori

Retinitis Punctata Albescens

Alport’s Syndrome

Drug Toxicities Crystalline Retinopathies

Inflammatory Diseases

Tumors Choroidal Nevus

Trauma

Peripheral Retinal Diseases Uveal Effusion Syndrome

Vitreous

Other Type II Glomerulonephritis

continued

Page 5: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

74 C H A P T E R 3 Clinical Features of Retinal Disease

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Intraretinal Lipid Exudates Macular AtrophyHemorrhages

Macular Diseases Age-Related Macular Age-Related MacularDegeneration Degeneration

Chronic Central Serous Angioid StreaksChorioretinopathy

Central SerousChorioretinopathy

Myopic Degeneration

Chronic CME

Macular Phototoxicity

Pattern Dystrophy

Retinal Vascular Diseases Diabetic Retinopathy Diabetic Retinopathy

Hypertensive Retinopathy Hypertensive Retinopathy

Branch Retinal Vein Branch Retinal Vein Occlusion Occlusion

Central Retinal Vein Central Retinal Vein Occlusion Occlusion

Leukemic Retinopathy Juxtafoveal Retinal Telangiectasis

Radiation Retinopathy Radiation Retinopathy

Anemia Retinal Arterial Macroaneurysm

Ocular Ischemic Coat’s Disease Syndrome

Retinal Arterial Macroaneurysm

Sickle Cell Retinopathy

Bone Marrow Transplantation

High-altitude Sickness

Page 6: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 75

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Intraretinal Lipid Exudates Macular AtrophyHemorrhages

Hereditary Disorders Retinitis Pigmentosa Stargardt Disease

Best’s Disease

North Carolina MacularDystrophy

Sorsby’s Macular Dystrophy

Choroideremia

Gyrate Atrophy

Cone Dystrophy

Rod-Cone Degeneration

Drug Toxicities Intraocular Gentamicin Chloroquine/Hydroxychloroquine

Inflammatory Diseases HIV Retinopathy POHS

CMV Retinitis Toxoplasmosis

Sarcoidosis Multifocal Choroiditis

Behçet’s Disease Serpiginous Choroiditis

Tumors Choroidal Melanoma

Retinal Capillary Hemangioma

Trauma Blunt Trauma Chronic Retinal Detachment Commotio Retinae

Shaken Baby Syndrome Choroidal Rupture

Valsalva Retinopathy

Terson’s Syndrome

Purtscher’s Retinopathy

Peripheral Retinal Diseases Vitreoretinal Traction Retinal Detachment Syndrome

Retinal Tear/Detachment

Vitreous Posterior Vitreous Detachment

Other Laser Photocoagulation

continued

Page 7: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

76 C H A P T E R 3 Clinical Features of Retinal Disease

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Optic Disc Edema with Peripheral Pigment Epithelial Macular Star Pigmentation Detachment

Macular Diseases Central Serous Age-Related MacularChorioretinopathy Degeneration

Central SerousChorioretinopathy

Polypoidal ChoroidalVasculopathy

Retinal Vascular Diseases Hypertensive Retinopathy

Hereditary Disorders Retinitis Pigmentosa

Stargardt Disease

Pigmented Paravenous Retinochoroidal

Drug Toxicities Chloroquine Toxicity

Siderosis

Inflammatory Diseases Cat Scratch Disease DUSN

Toxoplasmosis Viral Retinitis

Lyme Disease

Syphilis

Tuberculosis

Polyarteritis Nodosa

Tumors Optic Disc Capillary BDUMP Hemangiomas

Trauma Commotio Retinae

Choroidal Rupture

Peripheral Retinal Diseases Choroidal Effusion (late)

Chronic Retinal Detachment

Reticular Pigmentary Degeneration

Lattice Degeneration

Vitreous

Other Papilledema Scatter Laser Optic Neuropathy Photocoagulation

Page 8: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 77

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Pigmented Lesions Preretinal Hemorrhage Retinal Crystals

Macular Diseases

Retinal Vascular Diseases Juxtafoveal Retinal Diabetic Retinopathy Juxtafoveal Retinal Telangiectasis Telangiectasis

Sickle Cell Retinopathy Branch Retinal Vein Sickle Cell Retinopathy(Black Sunburst) Occlusion

Sickle Cell Retinopathy

Leukemic Retinopathy

Retinal Arterial Macroaneurysm

Hereditary Disorders X-Linked Juvenile Bietti’s Crystalline RetinalRetinoschisis Dystrophy

Cystinosis

Hyperoxaluria

Drug Toxicities Tamoxifen Toxicity

Canthaxanthine Toxicity

Talc Retinopathy

Inflammatory Diseases Toxoplasmosis (inactive scar)

Tumors Choroidal Nevus

Choroidal Melanoma

CHRPE

Bear Tracks

Melanocytoma

Trauma Terson’s Syndrome

Valsalva Retinopathy

Shaken Baby Syndrome

Peripheral Retinal Diseases Retinal Tear

Vitreous Posterior Vitreous Detachment

Other

continued

Page 9: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

78 C H A P T E R 3 Clinical Features of Retinal Disease

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Retinal Retinitis RubeosisNeovascularization

Macular Diseases

Retinal Vascular Diseases Diabetic Retinopathy Diabetic Retinopathy

Branch Retinal Vein Central Retinal ArteryOcclusion Occlusion

Radiation Retinopathy Central Retinal Vein Occlusion

Sickle Cell Retinopathy Ocular Ischemic Syndrome

Retinopathy of Prematurity Coat’s Disease

Leukemic Retinopathy Radiation Retinopathy

FEVR Retinopathy of Prematurity

Eale’s Disease

Hereditary Disorders Norrie’s Disease

Incontinentia Pigmenti

Drug Toxicities Talc Retinopathy

Inflammatory Diseases Eale’s Disease Toxoplasmosis

Pars Planitis CMV Retinitis

Sarcoidosis HSV Retinitis

Acute Retinal Necrosis

PORN

Cat Scratch Disease

Toxocariasis

Syphilis

Fungal Chorioretinitis

Behçet’s Disease

Tumors Retinoblastoma

Choroidal Melanoma

Trauma

Peripheral Retinal Diseases Chronic Retinal Detachment Chronic Retinal Detachment

Vitreous CNS Lymphoma

Other

Page 10: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 79

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Subretinal Fluid Vasculitis Vitelliform Lesions

Macular Diseases Age-Related Macular Age-Related MacularDegeneration Degeneration

Central Serous Pattern DystrophiesChorioretinopathy

Retinal Vascular Diseases Coat’s Disease Eale’s Disease

Toxemia of Pregnancy Ocular Ischemic Syndrome

Hereditary Disorders Best’s Disease

Drug Toxicities

Inflammatory Diseases Vogt-Koyanagi-Harada Behçet’s DiseaseSyndrome

Posterior Scleritis Sarcoidosis

Systemic Lupus Erythematosus

Pars Planitis/Multiple Sclerosis

Toxoplasmosis

Syphilis

Tuberculosis

Viral Retinitis/ARN

Toxocariasis

Birdshot Chorioretinopathy

Lyme Disease

Leukemic/Lymphoma

Frosted Branch Angiitis

Tumors Choroidal Melanoma

Choroidal Hemangioma

Choroidal Metastasis

Trauma

Peripheral Retinal Diseases

Vitreous Idiopathic Vitritis

CNS Lymphoma

Other Optic Pit

continued

Page 11: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

80 C H A P T E R 3 Clinical Features of Retinal Disease

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Vitreous Hemorrhage White-Centered White Dot SyndromesHemorrhages

Macular Diseases Age-Related Macular DrusenDegeneration

Retinal Vascular Diseases Diabetic Retinopathy Diabetic Retinopathy

Branch Retinal Vein Occlusion

Sickle Cell Retinopathy Leukemic Retinopathy

Leukemic Retinopathy Hypertensive Retinopathy

Retinal Arterial AnemiaMacroaneurysm

Eale’s Disease

Coat’s Disease

Peripapillary Arterial Loops

Retinopathy of Prematurity

Hereditary Disorders X-Linked Juvenile Stargardt DiseaseRetinoschisis

Fundus Albipunctatus

Retinitis Punctata Albescens

Flecked Retina of Kandori

Drug Toxicities

Page 12: Clinical Features of Retinal Disease · Tumors Trauma Commotio Retinae Peripheral Retinal Diseases Vitreous ... Toxemia of Pregnancy Ocular Ischemic Syndrome Hereditary Disorders

C H A P T E R 3 Clinical Features of Retinal Disease 81

T A B L E 1

Clinical Features of Retinal Disease (cont’d)

Vitreous Hemorrhage White-Centered White Dot SyndromesHemorrhages

Inflammatory Diseases Sarcoidosis HIV Retinopathy APMPPE

Pars Planitis Candida MEWDS Endophthalmitis DUSN

Toxoplasmosis Multifocal Choroiditis

Serpiginous Choroiditis

Birdshot Chorioretinitis

Sarcoidosis

Histoplasmosis

Pneumocystis Choroidopathy

Behçet’s Disease

Toxoplasmosis

Sympathetic Ophthalmia

Syphilis

Tumors

Trauma Terson’s Syndrome Shaken Baby Syndrome

Shaken Baby Syndrome Childbirth

Optic Disc Evulsion

Peripheral Retinal Diseases Retinal Tear/Detachment

Vitreous Posterior Vitreous Detachment Lymphoma

Other Subacute Bacterial Laser PhotocoagulationEndocarditis

Intracranial Hemorrhage

Carbon Monoxide Poisoning/Anoxia

continued